ʻO Chondrosarcome

ʻO Chondrosarcome

ʻO Chondrosarcoma kekahi o nā maʻi maʻi maʻi iwi mua loa i nā pākeke ma luna o 50 mau makahiki. Hiki ke ʻike ʻia ma nā pae like ʻole o ke kino. ʻO ka ʻoki ʻana ka mālama ʻana i ka koho mua.

He aha ka chondrosarcoma?

Ka wehewehe o chondrosarcoma

ʻO Chondrosarcoma kekahi ʻano o ka maʻi maʻi iwi. ʻO ka maʻi maʻi maʻi ke ʻano kikoʻī o ka hoʻomaka ʻana ma ka hui ʻana ma waena o nā iwi ʻelua ma ke kiʻekiʻe o ka cartilage articular (ʻiʻo maʻalahi a kūpaʻa e uhi ana i nā hui).

Hiki i ka Chondrosarcoma ke ulu i loko o kekahi cartilage hui. ʻIke pinepine ʻia ma ka pae o:

  • nā iwi lōʻihi e like me ka femur (iwi ʻūhā), tibia (iwi wāwae), a me ka humerus (iwi lima);
  • iwi palahalaha e like me ka iwi kua, iwi aoao, iwi kuamoo a me ka iwi pelvic.

Ka hoʻokaʻawale ʻana o nā chondrosarcomas

Hiki ke hoʻokaʻawale ʻia nā maʻi maʻi e like me nā ʻāpana he nui.

No ka laʻana, hiki ke hoʻokaʻawale i ka chondrosarcoma mua mai ka chondrosarcoma lua. Ua ʻōlelo ʻia he lua ia ma muli o ka ulu ʻana o kekahi maʻi ʻaʻai.

Hoʻokaʻawale ʻia nā maʻi maʻi e like me ko lākou nui. Ke kamaʻilio nei mākou e pili ana i ka staging ma ka ʻōlelo lapaʻau. ʻIke ʻia ka nui o ka maʻi maʻi iwi i ʻehā mau pae. ʻO ke kiʻekiʻe o ka pae, ʻoi aku ka nui o ka maʻi kanesa i laha ma ke kino.

I ka hapanui o nā hihia, aia nā chondrosarcomas i nā pae haʻahaʻa. ʻO ka pae 1 a hiki i ka 3 e pili ana i nā palapala kūloko. Hōʻike ka pae 4 i nā ʻano metastatic: ua neʻe nā cell cancer i nā hale ʻē aʻe o ke kino.

Hoʻomaopopo: ʻaʻole pili ka hana ʻana o ka maʻi ʻaʻai iwi i nā tumors i ka iwi kuamoo a me nā pelvis.

ʻO nā kumu o ka chondrosarcoma

E like me nā ʻano maʻi maʻi ʻē aʻe, ʻo ka chondrosarcomas kahi kumu i hoʻomaopopo ʻole ʻia.

I kēia lā, ua ʻike ʻia ʻo ka hoʻomohala ʻana o ka chondrosarcoma ma muli o:

  • nā maʻi maʻi iwi (non-cancerous) e like me chondroma a i ʻole osteochondroma;
  • bilin retinoblastoma, kahi ʻano maʻi ʻaʻai maka;
  • Maʻi ʻo Paget, he maʻi iwi maikaʻi;
  • ʻO Li-Fraumeni syndrome, kahi kūlana maʻamau i predisposing i nā ʻano tumors.

ʻO ka diagnostics o chondrosarcome

Hiki ke kānalua ʻia kēia ʻano maʻi kanesa ma nā hihia i ʻōlelo ʻia ma luna, a i ʻole ma ke alo o kekahi mau hōʻailona lapaʻau. Hiki ke hōʻoia a hoʻonui ʻia ka ʻike o ka chondrosarcoma e:

  • nā hoʻokolohua kiʻi lapaʻau e like me x-ray, CT scans, magnetic resonance imaging (MRI) a me ka iwi scintigraphy;
  • kahi biopsy e komo ana i ka lawe ʻana i kahi ʻāpana o ke kiko no ke kālailai ʻana, keu hoʻi inā kānalua ʻia ka maʻi ʻaʻai.

Hiki ke hoʻohana ʻia kēia mau hoʻāʻo e hōʻoia i ka ʻike o ka osteosarcoma, e ana i kona nui a nānā i ka loaʻa a me ka ʻole o nā metastases.

Nā kānaka e pili ana

Hoʻomaʻamaʻa pinepine ʻia nā Chondrosarcomas i nā pākeke ma mua o 50. Hiki naʻe ke ʻike ʻia kēia mau maʻi maʻi mai ka makahiki kanakolu. ʻAʻole ʻike ʻia lākou i nā keiki a me nā ʻōpio.

Nā hōʻailona o ka chondrosarcoma

Paena kaona

ʻO ka ʻeha iwi ka hōʻailona mua o ka maʻi ʻaʻai iwi. Hiki ke hoʻomau a kuewa paha ka ʻeha, ʻoi aku a ʻoi ʻole o ka ikaika, localized a diffuse paha.

Huʻi kūloko

ʻO ka hoʻomohala ʻana o ka chondrosarcoma hiki ke alakaʻi i ke ʻano o kahi puʻupuʻu a palpable mass i loko o ka ʻiʻo i hoʻopilikia ʻia.

Nā hōʻailona pili ʻē aʻe

Hiki ke hele pū ʻia ka ʻeha me nā hōʻailona ʻē aʻe e pili ana i ka wahi, ke ʻano a me ke ʻano o ka maʻi kanesa. O kahi laʻana :

  • nā maʻi kaʻa, ʻoi aku ka paʻakikī o nā iwi o ke pelvis;
  • pilikia hanu ke ulu ka ma'i ma'i ma ka iwi aoao.

Nā lāʻau lapaʻau no ka chondrosarcoma

Hoʻolā hewa

ʻO ka ʻoki ʻana ka mālama ʻana i ka koho mua. Hiki i ka hana ke hoʻohana i nā ʻano like ʻole me:

  • ʻO ka wehe ʻana o ka ʻōpū me kahi ʻāpana o ka iwi a me nā ʻiʻo maʻamau e puni ana;
  • ʻo ka curettage, ʻo ia ka wehe ʻana i ke koko ma ke ʻoki ʻana me ka ʻole o ka iwi.

ʻO ke kelepona

Hoʻohana kēia ʻano hana i ka radiation e luku ai i nā maʻi maʻi maʻi. Manaʻo ʻia i ka wā ʻaʻole hiki ke wehe ʻia ka chondrosarcoma e ka ʻoki.

ʻOki kino a me ka chemotherapy

Ke paʻakikī ka chondrosarcoma, hiki ke noʻonoʻo ʻia ka chemotherapy me ka hoʻohui ʻana i ke kaʻina. Hoʻohana ka lāʻau kemotherapy i nā kemika e hoʻōki i ka ulu ʻana o nā maʻi kanesa.

immunotherapy

He ala hou kēia no ka mālama ʻana i ka maʻi ʻaʻai. He mea kōkua paha a i ʻole he koho ʻē aʻe i nā hana i ʻōlelo ʻia ma luna. Ke hoʻomau nei ka noiʻi. ʻO ka pahuhopu o ka immunotherapy e hoʻonāukiuki i nā pale pale pale o ke kino e hakakā i ka ulu ʻana o nā hunaola maʻi ʻaʻai.

Kāohi i ka chondrosarcoma

ʻAʻole maopopo i ke kumu o chondrosarcomas. ʻO ka ʻōlelo maʻamau, ʻo ka pale ʻana i ka maʻi kanesa e hilinaʻi nei i ka mālama ʻana i ke ola olakino.

Paipai ʻia hoʻi e ʻimi i nā ʻōlelo aʻoaʻo olakino i kahi kānalua iki. Paipai ka hōʻike mua i ka hoʻomaʻamaʻa kūleʻa a palena i ka makaʻu o nā pilikia.

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