Reye maʻi maʻi
He aha kēīa ?
ʻO Reye's Syndrome kahi maʻi maʻi ʻole ʻole e hiki ke hōʻeha i ka ake a me ka lolo. Inā mālama ʻole ʻia ka maʻi, hiki iā ia ke hōʻino i ka lolo a i ʻole hiki ke make no kēlā kanaka kēia kanaka.
ʻO nā kumuhana i loli pinepine ʻia e Reye's Syndrome nā keiki a me nā ʻōpio ʻōpio ma lalo o ka makahiki 20. Eia nō naʻe, ua ʻike ʻia nā hihia o nā ʻelemākule. (1)
ʻO ka laha o kēia pathology ma Palani (ka helu o nā hihia o ka maʻi i kahi manawa i hāʻawi ʻia, i kahi heluna kanaka i hāʻawi ʻia) he 0.08 mau hihia no 100 mau keiki.
Ua waiho ʻia kahi loulou kumu a me ka hopena i ka United States ke lawe i ka aspirin a me ka ulu ʻana o Reye's Syndrome.
A laila loiloi ʻia kēia pilina ma Palani (ma waena o 1995 a me 1996). Ua ʻae ka hope i ka helu kanaka o 8 mau keiki ma lalo o 15 mau makahiki e ʻeha nei i kēia maʻi a lawe i ka aspirin. ʻO ka nīnau no ka lakio pōmaikaʻi / pōpilikia o ka aspirin ʻaʻole naʻe i maikaʻi me ka ʻole o kahi ʻōlelo aʻoaʻo. ʻO kēia kikoʻī i ka kuhikuhi o ka aspirin e pili ana i nā keiki me nā maʻi viral, e like me ka moa, influenza, etc.
I kēia ʻano, ua hoʻokumu ka ANSM (National Agency for Health and Medicines) i ka ʻoiaʻiʻo ʻaʻole pono e hāʻawi ʻia ka acetylsalicylic acid (aspirin) i nā keiki e ʻeha nei i kēia ʻano maʻi inā ʻaʻole i holo pono nā hana ʻē aʻe. . Eia hou, i ka hanana o ka luaʻi, nā maʻi neurological, nā haunaele o ka ʻike a me nā hana maʻamau ʻole, pono e hoʻopau ʻia kēia lapaʻau. (3)
Ōuli
ʻO nā ʻōuli i pili pinepine ʻia me ka Reye's Syndrome: (1)
- ka luaʻi no ke kumu kumu ʻole;
- molowa: nele i ka hoihoi, hoihoi a me ka ikaika;
- hiamoe;
- hoʻonui i ka hanu;
- ka hopu epileptic.
Hōʻike pinepine ʻia kēia mau hōʻailona "laulaha" he mau lā wale nō ma hope o ka maʻi viral.
I kekahi mau hihia, hiki i kēia mau ʻōuli mua ke holomua i nā mea ʻoi aku ke koʻikoʻi: (1)
- nā maʻi pilikino: hoʻonāukiuki, hoʻonāukiuki, hana kolohe, a pēlā aku.
- kahi mokuʻāina a me ka hopohopo i hiki ke hoʻohui ʻia i kekahi manawa me nā hallucination;
- nalowale o ka ʻike e hiki ai i kahi koma.
ʻO ke kūkākūkā ʻana o kahi kauka e pono ai i ka wanaʻao ke kānalua no kēia maʻi i ke keiki.
ʻOiai ʻaʻole pili kēia ʻano o nā ʻōuli me Reye's Syndrome, pono e hōʻoia i ke kuhiakau i mea e hōʻoia ai ʻaʻole ka ulu ʻana o ka pathology. I kēia hihia, he mea nui ia e aʻoaʻo aku i ke kauka no ke komo ʻana o ka aspirin i ka wā kamaliʻi e pili ana i ka ulu ʻana o kēia maʻi. Eia kekahi, inā ʻaʻohe palapala a ke keiki no ka lawe ʻana i ka aspirin ma mua, hiki ke kāpae ʻia ka hiki o ka ulu ʻana o ka maʻi. (1)
Nā kumu o ka maʻi
ʻAʻole ʻike ʻia ke kumu pono o Reye's Syndrome. Eia nō naʻe, ʻo ka hapa nui o nā maʻi e pili ana i nā keiki a me nā ʻōpio (ma lalo o 20 mau makahiki) e hoʻi hou ana mai kahi maʻi viral, a ʻoi aku ka nui o ka maʻi influenza a me ka moa. Eia hou, ua loaʻa i kēia mau mea maʻi kahi lāʻau lapaʻau no aspirin i ka mālama ʻana i kēia maʻi viral. I kēia ʻano, ʻo ka mālama ʻana me ka aspirin o kahi virosis ka mea i loaʻa pinepine i ke kumu.
ʻO kahi mea hou aʻe i ka hoʻomohala ʻana o kēia pathology hopena i nā hale liʻiliʻi i loko o nā hunaola: ka mitochondria, nā mea i hōʻino ʻia.
Hāʻawi kēia mau kūkulu pūnaewele i ka ikehu e pono ai no ka ulu ʻana o ka pūnaewele. He mea nui lākou no ka hana kūpono o ke ake. ʻOiaʻiʻo, kānana pū ka mitochondria i nā toxins mai ke kahe o ke koko a pili pū kekahi i ke kaohi o ke kō kō (pae kō) i ke kino.
I loko o ka pōʻaiapili kahi e hopena ai kēia mau ʻōnaehana hoʻoponopono hepatic, hiki ke luku ʻia ke akepaʻa. ʻO ka luku ʻia o ke ake ake ka hopena o ka hana ʻana o nā kemika ʻino. Ma ka hele ʻana i loko o ke kahe o ke koko, hiki i kēia mau toxins ke hōʻino i ka meaola āpau a me ka lolo. (1)
Hiki i nā maʻi ʻē aʻe ke kumu o nā ʻōuli e pili pū ana me ka maʻi Reye. I kēia ʻano, hiki ke hoʻoholo ʻia ke kuhi o kēia ʻano syndrome ma lalo o kekahi mau ʻano. ʻO kēia mau pathologies ʻē aʻe:
- meningitis: ka wela o nā membrane pale e uhi ana i ka lolo a me ka iwi kuamoʻo;
- encephalitis: ka hoʻohaunaele o ka lolo;
- nā maʻi e hui pū nei i nā maʻi metabolic e hoʻopili ana i nā hopena kemika o ka meaola. ʻO ka mea maʻamau: acyl-CoA kaulahao kaulahao dehydrogenase (MCADD).
Nā mea pilikino
ʻO ka mea nui pilikia no ka Reye's Syndrome ʻo ka lawe ʻana i ka aspirin ke mālama ʻana i ka maʻi flu-like me ka maʻi virus a i ʻole ka moa i nā keiki a i ʻole nā ʻōpio ʻōpio.
Kāohi a me ka lapaʻau
Hoʻomaka ka hōʻailona o kēia maʻi me kahi hōʻike ʻokoʻa ma ka nānā ʻana i nā ʻōuli i hōʻike ʻia e ka mea maʻi a me kāna mōʻaukala, e pili ana i ka lawe ʻana o ka aspirin i ka wā o ka mālama ʻana i kahi maʻi viral.
Hiki i ke kahe ʻana o ke koko a me ka mimi ke ʻae i ke kuhi o ka Reye's Syndrome i ke ʻano e hiki ke loaʻa nā toxins ʻano o ka pathology i loko o kēia kino wai. ʻO ke kū ʻana o kēia mau mea ʻino no ke kino kahi kumu o ka hana ate ʻole.
Hiki i nā hoʻokolohua ʻē aʻe ke lilo i mea o ka hōʻike o ka maʻi.
- ka scanner, e hiki ai ke kahakiʻi i nā pehu o ka lolo;
- kahi lumbar puncture, kahi o kahi laʻana o ka wai cerebrospinal i lawe ʻia mai ka iwi kuamoʻo a kālailai ʻia i mea e nānā ai i ka hiki ke loaʻa nā koʻohune a me nā mea ʻino paha;
- kahi biopsy ate, kahi i lawe ʻia ai kahi laʻana o ke akepaʻa akepaʻa a nānā ʻia ma lalo o kahi microscope e hoʻoholo ai i ke alo a i ʻole ka loaʻa ʻole o nā hunaola e pili ana me ka Reye's Syndrome.
Pono e hoʻokō ʻia ka mālama ʻana i ka maʻi i ka wā e hana ʻia ai ke kuhi.
ʻO ka pahuhopu o ka mālama ʻana e hoʻoliʻiliʻi i nā ʻōuli a ʻae i nā mea ola e hana i kā lākou hana a pale pū hoʻi i ka lolo mai nā pōʻino i hiki i ka maʻi ke hana.
Hiki ke lawelawe ʻia kahi helu nui o nā lāʻau, ma ke ʻano maʻamau, e like me:
- nā electrolytes a me nā wai, e hiki ai ke hoʻihoʻi i ke kaulike o nā paʻakai, nā minelala a me nā meaola i loko o ke kino (ʻo ia hoʻi ka glycemia i ke kahe o ke koko);
- diuretics: e kōkua i ke ake i kāna hana;
- nā detoxifiers amonia;
- anticonvulsants, i ka mālama ʻana i ka hopu ʻana o ka maʻi epileptic.
Hoʻokomo ʻia paha ke kōkua kōkua hanu i kahi hoʻonohonoho kahi i paʻakikī ai ke keiki i kona hanu ʻana.
I ka manawa e emi ai ka pehu o ka lolo, hoʻi i nā hana nui a ke kino i ka maʻamau. (1)