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ʻO Amyotrophie
Wehewehe: he aha ka amyotrophy?
ʻO Amyotrophy kahi huaʻōlelo lapaʻau no ka ʻiʻo atrophy, ka emi ʻana o ka nui o ka ʻiʻo. E pili ana i nā ʻiʻo skeletal striated, ʻo ia nā ʻiʻo ma lalo o ka mana manuahi.
ʻO nā hiʻohiʻona o ka amyotrophy he loli. Ma muli o ka hihia, hiki i kēia atrophy muscle ke:
- kūloko a i ʻole laulā, 'o ia ho'i, hiki ke ho'opili i ka 'i'o ho'okahi, nā 'i'o a pau o ka hui 'i'o a i 'ole nā 'i'o a pau o ke kino;
- huʻi a mau paha, me ka hoʻomohala wikiwiki a lohi paha;
- hānau ʻia a loaʻa paha, 'o ia ho'i, hiki ke hana 'ia ma muli o kekahi 'ano 'ole mai ka hānau 'ana a i 'ole ma muli o ka ma'i i loa'a.
Nā wehewehe: he aha nā kumu o ka atrophy muscular?
Hiki ke loaʻa nā kumu like ʻole. Ma muli paha o:
- he hookui kino, ʻo ia hoʻi ka lōʻihi o ka immobilization o kahi ʻiʻo a i ʻole pūʻulu ʻiʻo;
- ʻo ka myopathy hoʻoilina, he maʻi hoʻoilina e pili ana i nā ʻiʻo;
- loaʻa ka myopathy, he ma'i o na i'o nona ke kumu i hooili ole ia;
- pōʻino ʻōnaehana nerve.
ʻO ka hihia o ka immobilization kino
Hiki i ka immobilization kino ke alakaʻi i ka atrophy ma muli o ka nele o ka hana ʻiʻo. Hiki ke hoʻokuʻu ʻia ka ʻiʻo, no ka laʻana, ma muli o ke kau ʻana o kahi kiola i ka wā haki. ʻO kēia atrophy, i kapa ʻia i kekahi manawa ʻo ka hoʻopau ʻana i ka ʻiʻo, he palupalu a hiki ke hoʻohuli.
ʻO ka hihia o ka myopathy hoʻoilina
ʻO nā myopathies o ke kumu hoʻoilina ke kumu o ka atrophy muscular. ʻO kēia ka hihia i nā muscular dystrophies, nā maʻi i hōʻike ʻia e ka degeneration o nā ʻiʻo ʻiʻo.
ʻO kekahi o nā kumu hoʻoilina o ka muscular atrophy penei:
- ʻO Duchenne muscular dystrophy, a i ʻole Duchenne muscular dystrophy, ʻo ia kahi maʻi maʻi ʻokoʻa i ʻike ʻia e ka holomua a me ka nui o ka hoʻohaʻahaʻa ʻana i ka ʻiʻo;
- ʻO ka maʻi o Steinert, ai'ole Steinert's myotonic dystrophy, 'o ia ka ma'i e hiki ke 'ike 'ia ma ke 'ano he amyotrophy a me myatonia (ka ma'i 'ino o ka io);
- facio-scapulo-humeral myopathy ʻo ia ka muscular dystrophy e pili ana i nā ʻiʻo o ka maka a me nā ʻiʻo o ke kāʻei poʻohiwi (e hoʻopili ana i nā lālā o luna i ke kumu).
ʻO ka hihia o ka myopathy i loaʻa
ʻO ka amyotrophy ka hopena o nā myopathies i loaʻa. Hiki i kēia mau maʻi ʻiʻo hoʻoilina ʻole ke kumu.
Hiki ke loaʻa nā myopathies i ke kumu inflammatory, i ka wā o:
- polymyosites i hōʻike ʻia e ka mumū o nā ʻiʻo;
- dermatomyosites ka mea i hōʻike ʻia e ka mumū o ka ʻili a me nā ʻiʻo.
ʻAʻole hiki i nā myopathies i loaʻa ke hōʻike i kekahi ʻano inflammatory. ʻO kēia ka hihia me nā myopathies okumu iatrogenic, ʻo ia hoʻi, nā maʻi ʻiʻo ma muli o ka lāʻau lapaʻau. No ka laʻana, i nā kiʻekiʻe kiʻekiʻe a i ka wā lōʻihi, hiki i ka cortisone a me kāna mau derivatives ke kumu o ka atrophy.
Nā kumu neurological o ka atrophy muscular
I kekahi mau hihia, hiki i ka atrophy ke kumu neurological. Hoʻokumu ʻia ka ʻāʻī o ka ʻiʻo ma muli o ka pōʻino o ka ʻōnaehana nerve. Hiki i kēia ke loaʻa kekahi mau wehewehe, e like me:
- la ʻO ka maʻi o Charcot, a i ʻole amyotrophic lateral sclerosis, ʻo ia ka maʻi neurodegenerative e pili ana i nā neurons kaʻa (nā neurons e pili ana i ka neʻe ʻana) a hoʻoulu i ka amyotrophy a laila maʻi maʻi holomua o nā ʻiʻo.
- ka amyotrophie iwi kuamoo, he ma'i ma'i like 'ole e hiki ke ho'opilikia i nā 'i'o o ke a'a o nā lālā (proximal spinal atrophy) a i 'ole nā 'i'o o nā wēlau o nā lālā (distal spinal atrophy);
- la poliomyelitis, he ma'i lele o ke kumu viral (poliovirus) hiki ke ho'oulu i ka atrophies a me ka lolo;
- nā hana hōʻino, hiki ke loaʻa i hoʻokahi a ʻoi aku paha nā aʻalolo.
Evolution: he aha ka makaʻu o nā pilikia?
ʻO ka ulu ʻana o ka muscular atrophy e pili ana i nā ʻāpana he nui e like me ke kumu o ka ʻiʻo atrophy, ke kūlana o ka mea maʻi a me ka hoʻokele olakino. I kekahi mau hihia, hiki ke hoʻonui a hoʻolaha ʻia ka atrophy muscular i nā ʻiʻo ʻē aʻe o ke kino, a i ʻole i ke kino holoʻokoʻa. I nā ʻano koʻikoʻi loa, hiki ʻole ke hoʻihoʻi ʻia ka atrophy muscle.
Lapaʻau: pehea e mālama ai i ka muscular atrophy?
Hoʻomaʻamaʻa ʻia ka mālama ʻana i ke kumu o ka atrophy muscular. Hiki ke hoʻokō ʻia ka lāʻau lapaʻau i ka wā o ka myopathy inflammatory. Hiki ke ʻōlelo ʻia nā manawa physiotherapy i ka wā o ka immobilization kino lōʻihi.