hale ana

hale ana

ʻO ka cavernoma kahi ʻino o kekahi mau aʻa koko. ʻO ka hihia maʻamau ka cerebral cavernoma, a i ʻole intracranial cavernoma. ʻAʻole ia he hōʻailona maʻamau akā hiki i kekahi manawa ke hoʻoulu i nā maʻi like ʻole e like me ke poʻo, ka hopu a me nā maʻi neurological. Hiki ke noʻonoʻo ʻia ke ʻoki ʻana i nā hihia koʻikoʻi.

He aha ka cavernoma?

Ka wehewehe ʻana o ka cavernoma

ʻO ka cavernoma, a i ʻole cavernous angioma, he ʻano ʻino ia e kū nui ana i loko o ka ʻōnaehana nerve waena. ʻO ka hope i hana ʻia me ka lolo, ka cerebellum a me ka lolo i hoʻonui ʻia ma ke kuamoʻo i loko o ke kuamoʻo. No ka hōʻoia ʻana i ka hana ʻana o kēia ʻōnaehana, hānai ʻia e kahi pūnaewele o nā kīʻaha koko. I kekahi manawa, loaʻa i kekahi o kēia mau aʻa koko nā mea ʻino. Hoʻonui lākou a hoʻohui like ʻole i ke ʻano o nā lua liʻiliʻi, "caverns" a i ʻole cavernomas.

ʻO ka ʻoiaʻiʻo, ʻo ka cavernoma ke ʻano he pōpō o nā kīʻaha koko liʻiliʻi. Hiki ke hoʻomanaʻo ʻia kona ʻano maʻamau i kahi raspberry a i ʻole blackberry. Hiki ke ʻokoʻa ka nui o nā cavernomas mai kekahi mau millimeters a i kekahi mau kenimika.

ʻO ka huaʻōlelo lapaʻau "cavernoma" pili pinepine me ka cerebral cavernoma ka mea maʻamau. Aia kekahi mau maʻi kūikawā ʻē aʻe e like me ka medullary cavernoma i loaʻa i loko o ke kuamoʻo, a me portal cavernoma e kū ana ma waho o ka ʻōnaehana nerve waena.

Nā kumu o ka cavernoma

ʻAʻole maopopo i ke kumu o nā cavernomas a hiki i kēia lā. Ua ʻike ʻia naʻe kekahi i nā makahiki i hala iho nei. No ka laʻana, ua hiki i ka noiʻi ke hoʻokaʻawale i ʻelua ʻano o ka cerebral cavernomas:

  • ʻO ke ʻano ʻohana ma muli o ka hoʻololi hoʻoilina o ʻekolu mau genes (CCM1, CCM2 a me CCM3), e hōʻike ana i ka 20% o nā hihia a e hopena i ke alo o nā cavernomas me ka piʻi ʻana o nā pilikia;
  • ʻO ke ʻano sporadic, ʻaʻole ʻohana, ʻaʻole ia e hōʻike i kahi pōʻaiapili ʻohana a hopena i kahi cavernoma maʻamau.

ʻO ka ʻike ʻana o Cavernoma

Hoʻomaopopo ʻia ka loaʻa ʻana o kahi cavernoma cerebral ma nā hopena o kahi hoʻokolokolo hoʻohālikelike magnetic (MRI). Hiki i ke kauka ke kauoha i kahi angiogram e nānā i nā kīʻaha koko a me nā hoʻāʻo genetic e hōʻoia i kahi kumu hoʻoilina.

ʻO ka loaʻa ʻana o kahi cavernoma i hana pinepine ʻia no ka mea ʻaʻole i ʻike ʻia kēia hemahema. I nā huaʻōlelo ʻē aʻe, nui nā hihia o nā cavernomas hele ʻole ʻia.

Ka poʻe i hoʻopilikia ʻia e ka cavernoma

Hiki ke loaʻa ka cerebral cavernoma i nā kāne a me nā wahine i kēlā me kēia makahiki, ʻoiai ʻike pinepine ʻia ma waena o nā makahiki 20 a me 40.

He paʻakikī ka helu o nā hihia o ka cavernoma, ma muli o ka nele o nā hōʻailona ma ka hapa nui o nā hihia. Wahi a kekahi mau noiʻi, pili ka cerebral cavernomas ma kahi o 0,5% o ka lehulehu. Hōʻike lākou ma waena o 5% a me 10% o nā malformations vascular cerebral.

Nā hōʻailona o ka cavernoma

Ma 90% o nā hihia, ʻaʻohe hōʻailona i ʻike ʻia. ʻAʻole ʻike ʻia kahi cavernoma no ke ola. ʻIke ʻia ia i ka wā o kahi hoʻokolohua magnetic resonance imaging (MRI).

I nā hihia ʻē aʻe, hiki i kahi cerebral cavernoma ke hōʻike iā ia iho ma o:

  • epileptic seizures, me ka likelika ma waena o 40 a me 70%;
  • nā maʻi neurological me ka likelika ma waena o 35 a me 50%, hiki ke lilo i ka dizziness, ʻike pālua, nalowale koke o ka ʻike a me nā haunaele i ka naʻau;
  • nā poʻo poʻo me kahi kūpono o 10-30%;
  • nā hōʻike ʻē aʻe e like me ke ʻano o nā kiko ʻulaʻula ma ka ʻili.

ʻO ke koko ka pilikia nui o ka cavernoma. ʻO ka hapa nui o ka manawa, aia ke koko i loko o ka cavernoma. Eia nō naʻe, hiki ke hana ma waho o ka cavernoma a hoʻoulu i ka hemorrhage lolo.

ʻO nā lāʻau lapaʻau ʻo Cavernoma

Nā hana pale

Inā ʻaʻole ʻike ʻia nā hōʻailona a ʻaʻole i ʻike ʻia ka pilikia o ka hoʻopiʻi ʻana, lawe ʻia nā hana pale wale. ʻO kēia ka pale ʻana i nā haʻalulu i ke poʻo a me ka hoʻomaʻamaʻa ʻana i ke kahe koko. Hiki ke kuhikuhi ʻia nā lāʻau e hoʻemi i ke koko.

Nā hōʻailona hōʻailona

Inā loaʻa nā hōʻailona, ​​hiki ke hāʻawi ʻia nā lāʻau lapaʻau e hoʻomaha iā lākou. O kahi laʻana :

  • nā lāʻau anti-epileptic i ka hihia o ka hopu ʻana;
  • lāʻau ʻeha no ka ʻeha poʻo.

ʻO Neurosurgery

ʻO ka hopena wale nō i ka hoʻopau ʻana i ka cavernoma ʻo ke ʻokiʻoki. Manaʻo ʻia kēia hana ʻoki kino nui i nā hihia koʻikoʻi loa.

ʻO Radiosurgery

Hiki ke noʻonoʻo ʻia ke ʻano o ka radiotherapy no nā cavernomas liʻiliʻi a / a i ʻole hiki ke hoʻohana ʻia. Hoʻokumu ʻia ia ma ka hoʻohana ʻana i kahi kukuna o ka radiation i ke kuhikuhi o ka cavernoma.

Kāohi i ka cavernoma

ʻAʻole maopopo i ke kumu o nā cavernomas. Nui nā hihia i ʻōlelo ʻia he kumu genetic. ʻOiaʻiʻo, ʻaʻole hiki ke hoʻokumu ʻia kahi mea pale.

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