Ua hoʻopakele ke ʻano hana hou i ke ola o ke keiki

ʻOi aku ka nui o nā mea i ʻōlelo ʻia e pili ana i nā mea hiki ʻole o ka lāʻau lapaʻau. Ua hoʻohana ʻia kēia ʻano ʻano ʻōpio e nā kauka Parisian i kahi keikikāne me ka anemia congenital sickle cell anemia. ʻO ka puke "New England Journal of Medicine" i hōʻike e pili ana i ka holomua o nā loea.

Ua hana ʻia ke kaʻina hana he 15 mau mahina aku nei i kahi keikikāne 13 makahiki me ka maʻi maʻi maʻi anemia. Ma muli o ka maʻi, ua wehe ʻia kona ʻāʻī a ua hoʻololi ʻia nā ami ʻūhā ʻelua me nā mea hana. Pono ʻo ia e hoʻokahe koko i kēlā me kēia mahina.

ʻO ka maʻi maʻi sickle cell anemia. Hoʻololi ka gene defect i ke ʻano o nā keʻena koko ʻulaʻula (ʻulaʻula koko ʻulaʻula) mai ka poepoe a hiki i ka ʻokikiwi, kahi e hoʻopili pū ai lākou a kaʻa i loko o ke koko, e hōʻino ai i nā ʻōpū a me nā ʻiʻo o loko a lilo lākou i oxygenated. ʻO kēia ka hopena i ka ʻeha a me ka make mua ʻana, a pono pū kekahi e hoʻōla i ke koko.

Ua wehe ʻo Hôpital Necker Enfants Malades ma Paris i ke kīnā o ke keiki, ʻo ka mua ma ka luku ʻana i kona iwi iwi, kahi i hana ʻia ai. A laila hana hou lākou mai nā pūnaewele o ke keiki kāne, akā ua hoʻololi mua ʻia lākou i loko o ka hale hana. ʻO kēia kaʻina hana i hoʻokomo i ka gene kūpono i loko o lākou me ke kōkua o kahi maʻi. Ua hana hou ʻia ka iwi iwi e hana i nā ʻulaʻula maʻamau.

ʻO ke poʻo o ka noiʻi, prof. Ua haʻi ʻo Philippe Leboulch i ka BBC News e hana maikaʻi ana ke keikikāne, i kēia manawa he 15, a ʻaʻole ia e hōʻike i nā hōʻailona o ka maʻi maʻi anemia. ʻAʻole ʻo ia i manaʻo i nā hōʻailona a ʻaʻole pono ia i ka haukapila. Akā ʻaʻohe nīnau no ka hoʻōla piha ʻana. E hōʻoia ʻia ka maikaʻi o ka lāʻau lapaʻau e ka noiʻi hou a me nā hoʻāʻo ʻana i nā maʻi ʻē aʻe.

Manaʻo ʻo Kauka Deborah Gill mai ke Kulanui o Oxford ʻo ke kaʻina hana i hana ʻia e nā loea Farani he hana maikaʻi loa ia a he manawa kūpono no ka mālama pono ʻana i ka maʻi maʻi anemia.

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