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He aha ka hemochromatosis
ʻO Hemochromatosis (i kapa ʻia hemochromatosis a i ʻole hemochromatosis hoʻoilina) he ʻano hoʻoilina a hoʻoilina i kuleana ʻia no omo hao nui ma o ka ʻōpū a me kāna hoʻomāhuahua ma ke kino.
ʻO nā kumu o ka hemochromatosis
ʻO Hemochromatosis kahi maʻi maʻi i hoʻopili ʻia a hoʻololi o hoʻokahi a ʻoi paha nā ʻāpana. ʻIke ʻia kēia mau hoʻololi i nā wahi like ʻole o ka honua a kūlike kēlā me kēia i ka hōʻike ʻano ʻiʻī a koʻikoʻi paha o ka maʻi.
THEhemochromatosis hoʻoilina HFE (i kapa ʻia he type I hemochromatosis) ka ʻano maʻamau o ka maʻi. Pili ia i kahi hoʻololi i ka gen HFE ma chromosome 6.
ʻO ka pinepine o ka maʻi
ʻO Hemochromatosis kekahi o nā maʻi kūlohelohe maʻamau.
Ma kahi o 1 i 300 mau poʻe e halihali i nā kīnā genetika i predisposes i ka maʻi e hoʻomaka1. Akā ʻo ka mea e maopopo ai i kēia manawa hiki i ka maʻi ke loaʻa i kahi hōʻike olakino o ka loli pinepine a no laila ʻano laha ʻole nā ʻano hemochromatosis.
ʻO ka poʻe i hoʻopilikia ʻia e ka maʻi
ka na kanaka pili pinepine ʻia ma mua o nā wahine (3 kāne no 1 wahine).
Hōʻike pinepine ʻia nā ʻōuli 40 mau makahiki ma hope akā hiki ke hoʻomaka ma waena o 5 a 30 mau makahiki (hemochromatosis ʻōpio).
ʻIke pinepine ʻia ka maʻi i kekahi mau wahi o ka honua, e laʻa me ʻAmelika Hui Pū ʻIa a i ʻole ma ka ʻākau o ʻEulopa. ʻAʻole loaʻa ia ma nā ʻāina o Hikina Hema Asia a i ʻole ka lāhui ʻeleʻele.
I Palani, ʻoi aku ka nui o ka hopena o kekahi mau ʻāpana (Brittany).