Hoʻokumu ʻia ʻo Cerebellar ataxia e ka maʻi a ʻeha paha i ka cerebellum, aia i ka lolo. Hoʻohālikelike ʻia kēia maʻi e ka incoordination i nā neʻe o nā mākala. (1)

ʻO Ataxia ka manawa e hōʻuluʻulu pū nei i kekahi mau maʻi e pili ana i ka hoʻohui ʻana, ke kaulike a me ka ʻōlelo.

Hiki ke hoʻopili ʻia nā ʻāpana āpau o ke kino e ka maʻi, akā ʻo ka poʻe me ka ataxia he mau ʻano hemahema ko i:

- ke kaulike a me ka hele wāwae;

- ʻōlelo;

- ale ʻana;

- i ka hana ʻana i nā hana e koi ai i kahi kekelē o ka kaohi, e like me ke kākau ʻana a i ʻole ka ʻai ʻana;

- hihio.

Aia kekahi ʻano o ke ataxia i hōʻike ʻia e nā ʻōuli ʻokoʻa a me ke koʻikoʻi: (2)

- kiʻi ataxia ke ʻano i kūlike i ka hoʻomohala ʻana o nā ʻōuli ma ke ʻano he trauma, stroke, sclerosis, tumo lolo, deficiencies deficiencies a i ʻole nā ​​pilikia ʻē aʻe e hōʻino ana i ka lolo a me nā ʻōnaehana.

- ataxia hoʻoilina, kūlike i ke ʻano i ulu mālie ai nā ʻōuli (i loko o kekahi mau makahiki). ʻO kēia kumu ke kumu o nā genetical genities i hoʻoilina ʻia e nā mākua. Kapa ʻia kēia palapala he ataxia a Friedreich.

- idiopathic ataxia me ka hopena o ka cerebellar ataxia, kahi e loli iki ai ka lolo i ka manawa no nā kumu i ʻike pinepine ʻole ʻia.

No nā autxomal recessive cerebellar ataxia, he ʻāpana ia o kahi hui o nā maʻi neurological kakaikahi e hoʻopili i ka ʻōnaehana waena a me ke kikowaena. Hiki i kēia mau pathology ke hoʻopili i nā meaola ʻē aʻe. ʻO ke kumu o kēia ʻano maʻi he hoʻoilina hoʻoilina autosomal. A i ʻole ka lawe ʻia ʻana o kahi ʻāpana mutated o ka hoihoi mai nā mākua. ʻO ke kū hoʻokahi o kahi kope o ka moʻo e pono ai no ka ulu ʻana o ka maʻi.

Kū pinepine ka ulu ʻana o ka maʻi ma mua o ka makahiki 20.

He maʻi laha ʻole ia, ka laha o (nā helu o nā hihia i hāʻawi ʻia i kahi manawa i hāʻawi ʻia) aia ma waena o 1 a me 4 mau hihia no 100 mau kānaka. (000)

ʻO nā ʻōuli e pili pū ana me ka ataxia cerebellar he neurological a me mechanical.

Hoʻopilikia ka Cerebellar ataxia i ke kumu: mai ka ʻāʻī i nā hiʻupuʻu, akā ʻo nā lima a me nā wāwae kekahi.

ʻO nā ʻōuli laulā o ka cerebellar ataxia me: (1)

- hoʻonohonoho hoʻonohonoho clumsy (dysarthria): nā maʻi hui;

- nystagmus: neʻe pinepine i nā maka;

- nā neʻe maka ʻole i hoʻohui ʻia;

- kahi hele wāwae paʻa ʻole.

Hoʻololi ka Cerebellar ataxia i nā keiki ʻōpio o ka awelika o nā makahiki 3.

Hiki ke ulu ka maʻi ma hope o kekahi mau pule ma hope o ka maʻi viral. ʻO kēia mau maʻi viral i nīnau ʻia e komo pū me: chickenpox, infection with the Eptein-Barr virus, Coxsackie's disease or a infection with echovirus.

Pili paha nā kumu ʻē aʻe i kēia pathology, ma nā kikoʻī: (1)

- abscess i loko o ka cerebellum;

- ka inu ʻana i ka wai ʻona, kekahi mau lāʻau a i ʻole ka hoʻopili ʻana me nā insecticides;

- ke kahe o ka na i loko o ka cerebellum;

- mau sclerosis: hoʻomohala i nā mea hoʻopili i kahi meaola, e paʻakikī ana;

- kahi ulia vascular cerebral;

- kekahi mau lāʻau lapaʻau.

Pili pinepine ʻo Ataxia me ka hōʻino ʻana i ka cerebellum. Eia nō naʻe, ʻo nā mea ʻē aʻe i nā ʻāpana ʻē aʻe o ka ʻōnaehana hopohopo ke kumu.

Pili kēia ʻino i ka lolo me kekahi mau ʻano, e like me: kahi poʻo poʻo, ka nele o ka oxygen i ka lolo a i ʻole ka inu ʻana i ka waiʻona.

Eia hou, hiki ke lawe ʻia i ka maʻi ma o ka hoʻoilina hoʻoilina o ke ʻano autosomal. A i ʻole, ka hoʻolilo ʻia ʻana o kahi ʻāpana hoihoi o ka hoihoi, aia ma kahi chromosome moekolohe ʻole, mai nā mākua mai. ʻO ke kū hoʻokahi o nā kope ʻelua o ka gen mutated ka mea lawa i ka hoʻomohala ʻana o ka cerebellar ataxia. (2)

ʻO nā kumu pilikia e pili ana i ka cerebellar ataxia he genetic, i ka pōʻaiapili o ka hoʻoilina autosomal. I ka hihia hope, ua lawa ka lawe ʻana i hoʻokahi kope o ka genet mutated o ka hoihoi i ka ulu ʻana o ka maʻi i nā keiki. I kēia ʻano, inā pili kekahi o nā mākua ʻelua i ka maʻi pilikino, he 50% ka pilikia o ke keiki pēlā pū kekahi.

Hoʻokumu pū kekahi nā kumu ʻē aʻe i ka hoʻomohala ʻana o kēia pathology. Hoʻopili kēia i nā maʻi viral: ka moa, ka maʻi maʻi Eptein-Barr, ka maʻi ʻo Coxsackie a i ʻole kahi maʻi echovirus.

ʻO ka mea nui i ʻike nui ʻia i ka ataxia cerebellar ka lolo a me nā maʻi ʻōnaehana.

Hoʻohui pinepine ʻia ka ʻike mua o ka maʻi me kahi hōʻike ʻokoʻa, kahi e nīnau ai ke kauka i ka mea maʻi i nā nīnau he nui e hoʻoholo inā ua maʻi ʻo ia i kēia manawa. ʻO kēia manaʻo mua kekahi e hiki ai ke hoʻopau i nā kumu kūpono ʻē aʻe e pili ana i ke alo o nā hōʻailona.

Ma hope o kēia ʻike mua ʻana, hana ʻia nā hoʻokolokolo ʻana o ka lolo a me ka ʻōnaehana waena i mea e ʻike ai i nā wahi o ka cerebral cortex i hoʻopili ʻia e ka maʻi. Ma waena o kēia mau hoʻāʻo, hiki iā mākou ke ʻōlelo:

- ka scan o ke poʻo;

- MRI (Mākēneki Resonance Imaging) o ke poʻo.

Pili pono ka mālama ʻana i ka maʻi i ke kumu o ia: (1)

- pono ke kahakaha inā ʻo ke ataxia ka hopena o ke kahe ʻana o ka lolo;

- nā lāʻau e lahilahi ai ke koko i ka wā o ka hahau ʻana;

- nā lāʻauʻalopero a me nā antivirals i ka wā o nā maʻi;

- nā steroid no ka mālama ʻana i ka mumū o ka cerebellum.

Eia hou, i ke kumu o ke ataxia i hoʻokumu ʻia e kahi maʻi viral i hala iho nei, ʻaʻohe lāʻau e koi ʻia.

I ka hapanui o nā hihia o ka maʻi, ʻaʻohe mea e ola ai. ʻO nā lāʻau lapaʻau wale nō e kaohi a kaohi i nā hōʻailona ke kuhikuhi ʻia inā pono.

Hiki ke hoʻopili ʻia nā kōkua ʻōlelo, physiotherapy i ka hoʻonā ʻana o nā hemahema i ka neʻe ʻana, nā kau ʻoihana ʻoihana e ʻae ana i ka hana hou ʻana i nā hana o kēlā me kēia lā a i ʻole nā ​​lāʻau e ʻae ana i ka kaohi o nā mākala striated, nāʻiʻo caridaque, nā neʻe ocular a me ka mana urinary. (2)