ʻO Dermatomyositis kahi maʻi maʻi e hoʻopili i ka ʻili a me nā mākala. He maʻi maʻi autoimmune ka ʻike ʻole ʻia o kāna kumu, i hoʻokaʻawale ʻia i loko o ka hui o myopathies inflammatory idiopathic, a me kahi polymyositis. Hoʻololi nā pathology no nā makahiki me kahi wānana maikaʻi, i ka nele o nā pilikia koʻikoʻi, akā hiki ke pale i nā mākau kaʻa o ka mea maʻi. Ua koho ʻia he 1 i 50 a 000 i 1 mau kānaka e noho nei me ka dermatomyositis (ka laha ʻana) a ʻo ka helu o nā hihia hou i kēlā me kēia makahiki he 10 a 000 i kēlā me kēia miliona miliona (kona hanana). (1)

ʻO nā ʻōuli o dermatomyositis e like a like paha me nā mea e pili ana me nā myopathies hoʻouluhua ʻē aʻe: nā ʻili o ka ʻili, ʻehaʻeha a me nā nāwaliwali. Akā he mau mea e hiki ai ke hoʻokaʻawale i ka dermatomyositis mai nā myopathies hoʻoweliweli ʻē aʻe:

• ʻO nā pulu ʻulaʻula a hoʻomaʻemaʻe liʻiliʻi ma ka maka, ka ʻāʻī a me nā poʻohiwi ka mea maʻamau o nā hōʻike pilikino. ʻO ka hōʻino hiki i nā maka maka, i ke ʻano o nā aniani, ke ʻano.
• Hoʻopili ʻia nā mākala me ka symmetrically, e hoʻomaka ana mai ke kumu (ʻōpū, ʻāʻī, trapezius ...) ma mua o ka hiki ʻana, i kekahi mau hihia, nā lima a me nā wāwae.
• ʻO ke kūpono kiʻekiʻe o ka pili ʻana me ka maʻi ʻaʻai. Hoʻomaka ka hoʻomaka ʻana o kēia maʻi ʻaʻai i loko o nā mahina a i ʻole mau makahiki ma hope o ka maʻi, akā i kekahi manawa ke ʻike ʻia nā ʻōuli mua (hiki pū kekahi ma mua o lākou). ʻO ka maʻi ʻaʻai pinepine ia o ka umauma a i ʻole nā ​​ovaries no nā wahine a me ka akemāmā, prostate a me nā testes no nā kāne. ʻAʻole ʻae nā kumuwaiwai i ka makaʻu no ka poʻe me dermatomyositis o ke ulu ʻana i ka maʻi ʻaʻai (10-15% no kekahi, hoʻokahi hapakolu o nā poʻe ʻē aʻe). ʻO ka mea pōmaikaʻi, ʻaʻole pili kēia i ke ʻano ʻōpio o ka maʻi.

E hōʻoia a hōʻole paha kahi biopsy MRI a me nā muscle biopsy.

Hoʻomanaʻo ʻo dermatomyositis kahi maʻi e pili ana i ka hui o myopathies inflammatory idiopathic. ʻO ka adjective "idiopathic" ʻo ia hoʻi ʻaʻole ʻike ʻia ko lākou kumu. No laila, i kēia lā, ʻaʻole i ʻike ʻia ke kumu a me ke ʻano pololei o ka maʻi. E hopena ʻia paha ia mai ka hui pū ʻana o nā kūpuna a me nā ʻano kaiapuni.

Eia nō naʻe, ʻike mākou he maʻi autoimmune ia, ʻo ia hoʻi ke kumu o ka hoʻohaunaele ʻana o nā pale pale pale, e huli ana nā autoantibodies i ke kino, i kēia hihia e kūʻē i kekahi mau hunaola o nā mākala a me ka ʻili. E hoʻomaopopo naʻe, ʻaʻole ka poʻe āpau me ka dermatomyositis e hana i kēia mau autoantibodies. Hiki ke hoʻonāukiuki ʻia nā lāʻau, e like me nā virus. (1)

Hoʻopili pinepine ʻia nā wahine e dermatomyositis ma mua o nā kāne, ma kahi o ʻelua mau manawa. ʻO kēia ka hihia pinepine me nā maʻi autoimmune, me ka ʻike ʻole i ke kumu. Hiki ke ʻike ʻia ka maʻi i kēlā me kēia makahiki, akā ʻike ʻia ke ʻike ʻia ma waena o 50 a 60 mau makahiki. Me ka pili ʻana i ka dermatomyositis ʻōpio, aia ia ma waena o 5 a 14 mau makahiki i ʻike ʻia. Pono e hoʻokūpaʻa i kēia maʻi ʻaʻohe maʻi lele a hoʻoilina paha.

I ka loaʻa ʻole o ka hiki ke hana i nā kumu (ʻike ʻole ʻia) o ka maʻi, mālama nā lāʻau no ka dermatomyositis e hōʻemi / hoʻopau i ka hoʻowahāwahā ʻana ma o ka lawelawe ʻana i nā corticosteroids (corticosteroid therapy), a me ka hakakā ʻana i ka hana o autoantibodies i nā mea o nā lāʻau hoʻomalu immunomodulatory a i ʻole nā ​​lāʻau pale

Hiki i kēia mau ʻano hana ke kaupalena ʻia i ka ʻeha o ka ʻeha a me ka hōʻino, akā hiki i nā pilikia ke ala aʻe i ka hanana o ka maʻi ʻaʻai a me nā ʻano maʻi like ʻole (cardiac, pulmonary, etc.). Hiki i ka dermatomyositis ʻōpio ke kumu o nā pilikia digestive koʻikoʻi i nā keiki.

Pono nā mea maʻi e pale i ko lākou ʻili mai nā kukuna UV o ka lā, kahi e hoʻomāhuahua ai i nā ʻili o ka ʻili, ma o ka uhi ʻana i ka lole a me / a i ʻole ka pale lā ikaika. Ke hoʻokumu ʻia ke kuhi, pono ka mea hoʻomanawanui e hōʻike i nā hoʻokolohua kānana maʻamau no nā maʻi ʻaʻai e pili ana i ka maʻi.