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maʻi maʻi
ʻO ka huaʻōlelo ʻo dysmorfina e pili ana i nā malformations āpau a i ʻole deformations o nā kino o ke kino o ke kanaka (ate, iwi poʻo, nā mākala, a me nā mea ʻē aʻe). I ka hapa nui o nā hihia, aia kēia dysmorpia mai ka wā hānau. Hiki iā ia ke lilo i hōʻailona o kahi maʻi maʻi nui.
ʻO Dysmorpia, he aha ia?
Hoʻopili pū ʻo Dysmorfina i nā malformation āpau o ke kino o ke kanaka. Mai ka Greek "dys", ka paʻakikī, a me ka "morph", ke ʻano, koho ʻia kēia huaʻōlelo i nā ʻano ʻē aʻe o nā mea ʻino a i ʻole kekahi ʻāpana o ke kino. Nui a hewahewa ke ʻano o ka dismorphism. No laila, hiki i ka dysmorfina ke kuhikuhi like i kahi singular benign o kahi mea i loko o ke kanaka, ke hoʻohālikelike ʻia me ke koena o ka lehulehu, ma ke ʻano he anomaly koʻikoʻi.
'Lelo pinepine mākou e pili ana i ka dismorpia.
- Craniofacial dysmorfina
- Hepatic dysmorfina (o ke ake)
I ka hihia mua, ua ʻōlelo ʻia ʻo ka dismorpia he congenital, ʻo ia hoʻi mai ka wā hānau. ʻO kēia ka hihia no nā ʻaoʻao kiʻekiʻe o ka dysmorphic (ka helu o nā manamana lima i ʻoi aku ma mua o ka ʻumi, nā knuckles, a me nā mea ʻē aʻe.
Nā kumu
I ke kumu o ka congmital dysmorphias, hiki i nā kumu ke ʻokoʻa. ʻO nā helehelena pinepine ʻole ka hōʻailona o kahi maʻi maʻi, e like me trisomy 21 no kahi laʻana.
Hiki ke kumu i nā kumu:
- teratogenic a i waho paha (inu i ka wai ʻona, lāʻau a i ʻole hōʻike i nā kemika i ka wā hāpai a me nā mea ʻē aʻe.)
- infectious Via ka placenta (koʻohune, nā mea hoʻomaʻi, parasites)
- mīkini (kaomi ma ka fetus etc.)
- genetic (chromosomal me trisomies 13, 18, 21, hoʻoilina, a me nā mea ʻē aʻe)
- i ike ole
E pili ana i ka dysmorphism hepatic, ʻo ka hiʻohiʻona o kēia malformation e kū pū ʻia me cirrhosis. I kahi noiʻi i mālama ʻia ma 2004, i paʻi ʻia ma ka Ka Nupepa o Radiology: 76,6% o nā mea maʻi he 300 i ukali ʻia no ka cirrhosis i hōʻike ʻia i kekahi ʻano o ka hepatic dysmorphism.
PalekanaEND_LINK
Hana pinepine ʻia ka hōʻailona ma ka wā hānau e ka pediatrician ma ke ʻano he ʻāpana o ka ukali ʻana o ke keiki.
No nā mea maʻi me ka cirrhosis, ʻo ka maʻi maʻi kahi maʻi o ka maʻi. E kauoha ke kauka i kahi scan CT.
ʻO ka poʻe i pili a me nā kumu pilikia
Nā maʻi maʻi Craniofacial
ʻO nāforma hānau ʻole o nā kumu like ʻole, hiki iā lākou ke hoʻopili i nā keiki hānau hou. Eia nō naʻe, aia kekahi mau mea e hoʻonui i ka hiʻona o nā maʻi a i ʻole nā syndrome e pili ana i ka dismorfia:
- ka wai ʻona a hoʻohana lāʻau paha i ka wā hāpai
- ka hōʻike ʻana i nā kemika i ka wā hāpai
- ka launa pu ana
- nā pathologies hoʻoilina
ʻO kahi kumulāʻau ʻohana i hana ʻia e ka pediatrician a me nā mākua olaola ma luna o ʻelua a ʻekolu paha hanauna e koi ʻia e ʻike i nā mea pilikia.
Nā Dysmorphies hépathiques
Pono ka poʻe me ka cirrhosis e kiaʻi no ka dismorphism.
Nā ʻōuli o dysmorpia
Nui nā ʻōuli o ka congenital dysmorpia. E kiaʻi ke kauka maʻi maʻi:
No ka helehelena dysmorfina
- Ke ʻano o ka iwi poʻo, ka nui o nā fontanelles
- Alopecia
- Ke ʻano o nā maka a me ka mamao ma waena o nā maka
- Ke kinona a me ka ami o nā kuʻemaka
- Ke kinona o ka ihu (aʻa, alahaka ihu, piko a pēlā aku.)
- ʻO ka dimple ma luna o ka lehelehe e holoi ʻia i ka maʻi ʻalalā fetal
- Ke kinona o ka waha (lehelehe lepe, mānoanoa o nā lehelehe, ʻelemu, uvula, gums, alelo a me nā niho)
- ka auwae
- nā pepeiao: ke kūlana, ka hoʻonohonoho ʻana, ka nui, ka hemming a me ke ʻano
No nā dismorphias ʻē aʻe
- nā kihi: ka helu o nā manamana lima, knuckle a i ʻole fusion o nā manamana lima, nā manamana nui ʻole a pēlā aku.
- ka ʻili: nā ʻano ʻē pigmentation, nā wahi café-au-lait, nā kaha kau etc.
Nā hana no ka dismorpia
ʻAʻole hiki ke hoʻōla ʻia ʻo dysmorphias Congenital. ʻAʻohe lāʻau i hoʻomohala ʻia.
Akahai kekahi mau hihia o ka dysmorphism a ʻaʻole e koi i kahi lāʻau lapaʻau. Hoʻohana ʻia kekahi poʻe ma o ke kaha ʻana; ʻo kēia ka hihia no ka ami o nā manamana ʻelua e laʻa me.
I nā ʻano ʻoi loa o ka maʻi, pono e hele pū nā keiki me ke kauka i ko lākou ulu ʻana, a i ʻole e ukali paha i ka lāʻau lapaʻau e hoʻomaikaʻi ai i nā kūlana ola o ke keiki a i ʻole e hakakā kūʻē i ka pilikia e pili ana i ka dismorfia.
Kāohi i ka dismorotia
ʻOiai ʻaʻole ʻike ʻia ke kumu o ka dismorphism, ʻike pinepine ʻia i nā pilikia i ka wā hāpai i nā helu he nui.
No laila, he mea nui e hoʻomanaʻo i ka ʻai ʻana o ka waiʻona a i ʻole nā lāʻau i ka wā o ka hāpai ʻana e pāpā loa ʻia, ʻoiai i nā kau liʻiliʻi. Pono nā mea maʻi hāpai e nīnau mau i ke kauka ma mua o ka lawe ʻana i nā lāʻau.