ʻO Hyperlaxité

ʻO Hyperlaxité

He aha kēīa ?

ʻO Hyperlaxity kahi neʻe hui pū nui.

ʻO ke kūpaʻa a me ka ikaika o nā aʻa o loko o ke kino e hoʻokele ʻia e kekahi mau protein pili. I ke ʻano o ka hoʻololi ʻana i loko o kēia mau protein, ʻo nā mea ʻē aʻe e pili ana i nā ʻāpana paʻa o ke kino (nā hono, nā ʻāʻī, nā iwi a me nā ligament) e hoʻopili ʻia, e lilo i mea maʻalahi a palupalu a hiki ke hana i nā leona. No laila he artla hyperlaxity.

Ke alakaʻi nei kēia hyperlaxity i ka hyper-extension maʻalahi a ʻeha hoʻi o kekahi mau lālā o ke kino. ʻO kēia palupalu o nā lālā nā hopena pololei o kahi nāwaliwali a i ʻole ka ʻole o nā ligament a i kekahi manawa o ka nāwaliwali o ka iwi.

Pili kēia maʻi pilikino i nā poʻohiwi, kuʻe lima, nā pulima oʻu, nā kuli a me nā manamana lima. Hōʻike pinepine ʻia ʻo Hyperlaxity i ka wā kamaliʻi, i ka wā o ka hoʻomohala ʻana o nā pūnaewele hoʻopili.

Pili nā inoa ʻē aʻe i ka maʻi, ʻo lākou: (2)

- hypermobility;

- maʻi o nā ligament liʻiliʻi;

- maʻi maʻi hyperlaxity.

ʻOi aku ka maʻalahi o ka poʻe me ka hyperlaxity a ʻoi aku ka nui o ka haki o nā haʻi a me nā ligament dislocations i ka wā o sprains, nā luhi, a pēlā aku.

Hiki iā ia ke kaohi i ka makaʻu o nā pilikia i loko o ka pōʻaiapili o kēia pathology, ma nā kikoʻī:

- nā hoʻoikaika hoʻoikaika kino a me ka ligament;

- ke aʻo ʻana i ka "laulā maʻamau" o nā neʻe i mea e hōʻalo ai i nā hoʻolōʻihi hyper:

- pale i nā ligament i ka wā o ke kino, e hoʻohana ana i nā ʻōnaehana padding, nā pale kuli, a pēlā aku.

ʻO ka mālama ʻana i ka maʻi e pili ana i ka ʻeha a me ka hoʻoikaika ʻana i ka ligament. I kēia pōʻaiapili, pili pinepine ʻia kahi kuhikuhi o nā lāʻau (nā kalima, nā sprays, a pēlā aku.) (3)

Ōuli

ʻO Hyperlaxity kahi neʻe hui pū nui.

ʻO ke kūpaʻa a me ka ikaika o nā aʻa o loko o ke kino e hoʻokele ʻia e kekahi mau protein pili. I ke ʻano o ka hoʻololi ʻana i loko o kēia mau protein, ʻo nā mea ʻē aʻe e pili ana i nā ʻāpana paʻa o ke kino (nā hono, nā ʻāʻī, nā iwi a me nā ligament) e hoʻopili ʻia, e lilo i mea maʻalahi a palupalu a hiki ke hana i nā leona. No laila he artla hyperlaxity.

Ke alakaʻi nei kēia hyperlaxity i ka hyper-extension maʻalahi a ʻeha hoʻi o kekahi mau lālā o ke kino. ʻO kēia palupalu o nā lālā nā hopena pololei o kahi nāwaliwali a i ʻole ka ʻole o nā ligament a i kekahi manawa o ka nāwaliwali o ka iwi.

Pili kēia maʻi pilikino i nā poʻohiwi, kuʻe lima, nā pulima oʻu, nā kuli a me nā manamana lima. Hōʻike pinepine ʻia ʻo Hyperlaxity i ka wā kamaliʻi, i ka wā o ka hoʻomohala ʻana o nā pūnaewele hoʻopili.

Pili nā inoa ʻē aʻe i ka maʻi, ʻo lākou: (2)

- hypermobility;

- maʻi o nā ligament liʻiliʻi;

- maʻi maʻi hyperlaxity.

ʻOi aku ka maʻalahi o ka poʻe me ka hyperlaxity a ʻoi aku ka nui o ka haki o nā haʻi a me nā ligament dislocations i ka wā o sprains, nā luhi, a pēlā aku.

Hiki iā ia ke kaohi i ka makaʻu o nā pilikia i loko o ka pōʻaiapili o kēia pathology, ma nā kikoʻī:

- nā hoʻoikaika hoʻoikaika kino a me ka ligament;

- ke aʻo ʻana i ka "laulā maʻamau" o nā neʻe i mea e hōʻalo ai i nā hoʻolōʻihi hyper:

- pale i nā ligament i ka wā o ke kino, e hoʻohana ana i nā ʻōnaehana padding, nā pale kuli, a pēlā aku.

ʻO ka mālama ʻana i ka maʻi e pili ana i ka ʻeha a me ka hoʻoikaika ʻana i ka ligament. I kēia pōʻaiapili, pili pinepine ʻia kahi kuhikuhi o nā lāʻau (nā kalima, nā sprays, a pēlā aku.) (3)

Nā kumu o ka maʻi

ʻO ka hapa nui o nā hihia o hyperlaxity ʻaʻole pili i kekahi kumu kumu. I kēia hihia, he hyperlaxity maikaʻi.

Eia hou, hiki ke hoʻopili ʻia kēia pathology i:

- nā mea kūpono ʻole i ka hanana iwi, ke ʻano o nā iwi;

- nā mea kūponoʻole i ke kani a me ka paʻakikī o nāʻiʻo;

- ke alo o hyperlaxity i loko o ka ʻohana.

Kuhi kēia hihia hope loa i ka hiki i ka hoʻoilina i ka lawe ʻia ʻana o ka maʻi.

I nā hanana kakaikahi loa, nā hopena hyperlaxity mai ke ʻano o nā kūlana olakino. Pākuʻi ʻia kēia mau mea: (2)

- Down Syndrome, ʻike ʻia e ke kīnā ʻole o ka ʻike;

- cleidocranial dysplasia, ʻano e kahi maʻi hoʻoilina i ka ulu ʻana o nā iwi;

- Ehlers-Danlos Syndrome, ʻano e ka nui elasticity o ka nā mea hoʻopili;

- Marfan syndrome, ʻo ia hoʻi kahi maʻi pili pūnaewele;

- Morquio Syndrome, kahi maʻi hoʻoilina e pili ana i ka metabolism.

Nā mea pilikino

ʻAʻole ʻike maopopo ʻia nā mea weliweli no ka hoʻomohala ʻana i kēia maʻi.


Hiki i kekahi mau pathologies ke kumu o ka hopena o ke kumu o ka maʻi, e like me; Down syndrome, cleidocranial dysplasia, a pēlā aku. Akā, pili wale kēia mau ʻano i ka hapa liʻiliʻi o nā mea maʻi.

Eia hou, ua waiho ʻia kahi kānalua no ka lawe ʻia ʻana o ka maʻi i nā keiki i mua e nā ʻepekema. I kēia ʻano, hiki i ke alo o nā hoʻololi genetic no kekahi mau gen, i nā mākua, hiki ke hoʻolilo iā lākou i mea pilikia hou aʻe no ka hoʻomohala ʻana i ka maʻi.

Kāohi a me ka lapaʻau

Hana ʻia ke kuhi o ka maʻi ma ke ʻano ʻokoʻa, ke nānā aku i nā ʻano ʻano like ʻole.

ʻO ka hoʻokolohua Beighton a laila hiki i ka hiki ke nānā i ka hopena o ka maʻi i ka neʻe ʻana i nā mākala. Aia kēia hōʻike i kahi papa o 5 hōʻike. Pili kēia mau mea i:

- ke kūlana o ka poho o ka lima ma ka honua me ka mālama pono ʻana i nā wāwae;

- kūlou i kēlā me kēia kuʻe lima i hope;

- kūlou i kēlā me kēia kuli i hope;

- kūlou i ka manamana nui i mua o ka forearm;

- kūlou i ka manamana liʻiliʻi i hope ma mua o 90 °.

I loko o ka pōʻaiapili o kahi helu Beighton i ʻoi aku a i ʻole 4 paha, ʻeha paha ke kumuhana i ka hyperlaxity.

Pono paha kahi hōʻoia koko a me nā kukuna x i ke kuhi o ka maʻi. Hana ʻia kēia mau kiʻina hana e hōʻike i ka hoʻomohala ʻana o ka rheumatoid arthritis.

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