ʻO Hyperlaxité
He aha kēīa ?
ʻO Hyperlaxity kahi neʻe hui pū nui.
ʻO ke kūpaʻa a me ka ikaika o nā aʻa o loko o ke kino e hoʻokele ʻia e kekahi mau protein pili. I ke ʻano o ka hoʻololi ʻana i loko o kēia mau protein, ʻo nā mea ʻē aʻe e pili ana i nā ʻāpana paʻa o ke kino (nā hono, nā ʻāʻī, nā iwi a me nā ligament) e hoʻopili ʻia, e lilo i mea maʻalahi a palupalu a hiki ke hana i nā leona. No laila he artla hyperlaxity.
Ke alakaʻi nei kēia hyperlaxity i ka hyper-extension maʻalahi a ʻeha hoʻi o kekahi mau lālā o ke kino. ʻO kēia palupalu o nā lālā nā hopena pololei o kahi nāwaliwali a i ʻole ka ʻole o nā ligament a i kekahi manawa o ka nāwaliwali o ka iwi.
Pili kēia maʻi pilikino i nā poʻohiwi, kuʻe lima, nā pulima oʻu, nā kuli a me nā manamana lima. Hōʻike pinepine ʻia ʻo Hyperlaxity i ka wā kamaliʻi, i ka wā o ka hoʻomohala ʻana o nā pūnaewele hoʻopili.
Pili nā inoa ʻē aʻe i ka maʻi, ʻo lākou: (2)
- hypermobility;
- maʻi o nā ligament liʻiliʻi;
- maʻi maʻi hyperlaxity.
ʻOi aku ka maʻalahi o ka poʻe me ka hyperlaxity a ʻoi aku ka nui o ka haki o nā haʻi a me nā ligament dislocations i ka wā o sprains, nā luhi, a pēlā aku.
Hiki iā ia ke kaohi i ka makaʻu o nā pilikia i loko o ka pōʻaiapili o kēia pathology, ma nā kikoʻī:
- nā hoʻoikaika hoʻoikaika kino a me ka ligament;
- ke aʻo ʻana i ka "laulā maʻamau" o nā neʻe i mea e hōʻalo ai i nā hoʻolōʻihi hyper:
- pale i nā ligament i ka wā o ke kino, e hoʻohana ana i nā ʻōnaehana padding, nā pale kuli, a pēlā aku.
ʻO ka mālama ʻana i ka maʻi e pili ana i ka ʻeha a me ka hoʻoikaika ʻana i ka ligament. I kēia pōʻaiapili, pili pinepine ʻia kahi kuhikuhi o nā lāʻau (nā kalima, nā sprays, a pēlā aku.) (3)
Ōuli
ʻO Hyperlaxity kahi neʻe hui pū nui.
ʻO ke kūpaʻa a me ka ikaika o nā aʻa o loko o ke kino e hoʻokele ʻia e kekahi mau protein pili. I ke ʻano o ka hoʻololi ʻana i loko o kēia mau protein, ʻo nā mea ʻē aʻe e pili ana i nā ʻāpana paʻa o ke kino (nā hono, nā ʻāʻī, nā iwi a me nā ligament) e hoʻopili ʻia, e lilo i mea maʻalahi a palupalu a hiki ke hana i nā leona. No laila he artla hyperlaxity.
Ke alakaʻi nei kēia hyperlaxity i ka hyper-extension maʻalahi a ʻeha hoʻi o kekahi mau lālā o ke kino. ʻO kēia palupalu o nā lālā nā hopena pololei o kahi nāwaliwali a i ʻole ka ʻole o nā ligament a i kekahi manawa o ka nāwaliwali o ka iwi.
Pili kēia maʻi pilikino i nā poʻohiwi, kuʻe lima, nā pulima oʻu, nā kuli a me nā manamana lima. Hōʻike pinepine ʻia ʻo Hyperlaxity i ka wā kamaliʻi, i ka wā o ka hoʻomohala ʻana o nā pūnaewele hoʻopili.
Pili nā inoa ʻē aʻe i ka maʻi, ʻo lākou: (2)
- hypermobility;
- maʻi o nā ligament liʻiliʻi;
- maʻi maʻi hyperlaxity.
ʻOi aku ka maʻalahi o ka poʻe me ka hyperlaxity a ʻoi aku ka nui o ka haki o nā haʻi a me nā ligament dislocations i ka wā o sprains, nā luhi, a pēlā aku.
Hiki iā ia ke kaohi i ka makaʻu o nā pilikia i loko o ka pōʻaiapili o kēia pathology, ma nā kikoʻī:
- nā hoʻoikaika hoʻoikaika kino a me ka ligament;
- ke aʻo ʻana i ka "laulā maʻamau" o nā neʻe i mea e hōʻalo ai i nā hoʻolōʻihi hyper:
- pale i nā ligament i ka wā o ke kino, e hoʻohana ana i nā ʻōnaehana padding, nā pale kuli, a pēlā aku.
ʻO ka mālama ʻana i ka maʻi e pili ana i ka ʻeha a me ka hoʻoikaika ʻana i ka ligament. I kēia pōʻaiapili, pili pinepine ʻia kahi kuhikuhi o nā lāʻau (nā kalima, nā sprays, a pēlā aku.) (3)
Nā kumu o ka maʻi
ʻO ka hapa nui o nā hihia o hyperlaxity ʻaʻole pili i kekahi kumu kumu. I kēia hihia, he hyperlaxity maikaʻi.
Eia hou, hiki ke hoʻopili ʻia kēia pathology i:
- nā mea kūpono ʻole i ka hanana iwi, ke ʻano o nā iwi;
- nā mea kūponoʻole i ke kani a me ka paʻakikī o nāʻiʻo;
- ke alo o hyperlaxity i loko o ka ʻohana.
Kuhi kēia hihia hope loa i ka hiki i ka hoʻoilina i ka lawe ʻia ʻana o ka maʻi.
I nā hanana kakaikahi loa, nā hopena hyperlaxity mai ke ʻano o nā kūlana olakino. Pākuʻi ʻia kēia mau mea: (2)
- Down Syndrome, ʻike ʻia e ke kīnā ʻole o ka ʻike;
- cleidocranial dysplasia, ʻano e kahi maʻi hoʻoilina i ka ulu ʻana o nā iwi;
- Ehlers-Danlos Syndrome, ʻano e ka nui elasticity o ka nā mea hoʻopili;
- Marfan syndrome, ʻo ia hoʻi kahi maʻi pili pūnaewele;
- Morquio Syndrome, kahi maʻi hoʻoilina e pili ana i ka metabolism.
Nā mea pilikino
ʻAʻole ʻike maopopo ʻia nā mea weliweli no ka hoʻomohala ʻana i kēia maʻi.
Hiki i kekahi mau pathologies ke kumu o ka hopena o ke kumu o ka maʻi, e like me; Down syndrome, cleidocranial dysplasia, a pēlā aku. Akā, pili wale kēia mau ʻano i ka hapa liʻiliʻi o nā mea maʻi.
Eia hou, ua waiho ʻia kahi kānalua no ka lawe ʻia ʻana o ka maʻi i nā keiki i mua e nā ʻepekema. I kēia ʻano, hiki i ke alo o nā hoʻololi genetic no kekahi mau gen, i nā mākua, hiki ke hoʻolilo iā lākou i mea pilikia hou aʻe no ka hoʻomohala ʻana i ka maʻi.
Kāohi a me ka lapaʻau
Hana ʻia ke kuhi o ka maʻi ma ke ʻano ʻokoʻa, ke nānā aku i nā ʻano ʻano like ʻole.
ʻO ka hoʻokolohua Beighton a laila hiki i ka hiki ke nānā i ka hopena o ka maʻi i ka neʻe ʻana i nā mākala. Aia kēia hōʻike i kahi papa o 5 hōʻike. Pili kēia mau mea i:
- ke kūlana o ka poho o ka lima ma ka honua me ka mālama pono ʻana i nā wāwae;
- kūlou i kēlā me kēia kuʻe lima i hope;
- kūlou i kēlā me kēia kuli i hope;
- kūlou i ka manamana nui i mua o ka forearm;
- kūlou i ka manamana liʻiliʻi i hope ma mua o 90 °.
I loko o ka pōʻaiapili o kahi helu Beighton i ʻoi aku a i ʻole 4 paha, ʻeha paha ke kumuhana i ka hyperlaxity.
Pono paha kahi hōʻoia koko a me nā kukuna x i ke kuhi o ka maʻi. Hana ʻia kēia mau kiʻina hana e hōʻike i ka hoʻomohala ʻana o ka rheumatoid arthritis.