Pemphigus

Hōʻike ākea o ka maʻi

ʻO kēia kahi maʻi pilikino o ke kumu autoimmune e hoʻopili i ka ʻili a me nā membrane mucous. Hiki ke hoʻomohala ʻo Pemphigus i kēlā me kēia makahiki, akā naʻe, pili pinepine ia i nā kāne a me nā wahine i hele i ka mile nui 40-makahiki, ʻoi loa ka maʻi i nā poʻe 40-45 makahiki, a kākaʻikahi i nā keiki. ʻO ka mahele o ka pemphigus ma kahi o 1% o nā maʻi dermatological.

Nā kumu

ʻAʻole hiki ke hoʻokumu ʻia ka etiology o pemphigus no ka lōʻihi, akā ua hōʻoia ʻia e nā noiʻi ʻo ke kumu o kēia maʻi pilikino he hana maikaʻi ʻole ia o ka ʻōnaehana pale.^[3].

ʻO ka hana o ka ʻōnaehana pale pale no ka pale ʻana i nā meaola haole. Kū nā maʻi Autoimmune ke, i ka hopena o ka hana ʻole, hoʻouka ka ʻōnaehana pale i nā hunaola o ke kino, i ka hihia o pemphigus, ka ʻili. Hoʻopuka kuhi hewa nā ʻōpala i nā ʻōnaehana pale i nā protein i nā papa luna o ka ʻili olakino. ʻO nā Demosome, ʻo ia ka loulou pili i waena o nā hunaola o ka ʻili ma lalo o ka hoʻouka ʻana o autoantibodies, e nalowale i ko lākou pilina a luku ʻia, a hoʻopiha ʻia ka hakahaka hakahaka me ka wai intercellular, ma muli o kahi hopena i hoʻokumu ʻia ai nā vesicle acantholytic ka maʻi).

ʻO nā kumu pilikia no ka hoʻomohala ʻana i ka pemphigus hiki ke lilo i exogenous (nā maʻi infectious, nā virus, nā ʻoihana ʻoihana) a me nā kumu hopena, e like me ka predisposition genetical. ʻO nā kumu no ka hoʻomohala ʻana i ka pemphigus hiki ke lilo i haʻalulu ikaika nui, a me nā pathology o ka adrenal cortex.

ʻO nā limahana mahiʻai, ka mea pinepine e launa pū me nā lāʻau make a me nā insecticides, a me nā limahana i ka ʻoihana metala a me nā hale paʻi, e hoʻomohala i ka pemphigus.

Nā ʻano a me nā ʻōuli

ʻO nā hiʻohiʻona hiʻohiʻona o nā pathology i hōʻike ʻia he vesicle liʻiliʻi me nā mea serous, i hoʻopaʻa ʻia ma ke kino o ka mea maʻi, e like me ke ʻano o ka pemphigus.

• pelapela - ʻokoʻa i ka helehelena o nā huʻa me kahi huila lahilahi a me ka lapalapa i loko o ke kino. Me kahi ʻano pelapela a maʻamau paha, hoʻokuʻi ʻia nā huʻa i ka hoʻomaka o ka ulu ʻana o ka maʻi ma nā membrane mucous o ka ihu a me ka waha, no laila e hele nā ​​mea maʻi i ka kauka niho a mālama ʻia me ka kūleʻa ʻole, ka hoʻonele ʻana i ka manawa. Ke hopohopo nei nā mea maʻi e pili ana i ka hanu maikaʻi ʻole, ʻeha ma ka waha i ka wā e ʻai ana, e kamaʻilio ana a e ale ana i ka lihi. ʻAʻole ʻike pinepine ka poʻe maʻi i nā huʻupuʻu liʻiliʻi e hiki wawe i ka wehe ʻana, no laila ʻo ka hoʻopiʻi nui ka lū ʻia o ka ʻeha ma ka waha, kahi a nā kauka niho e kuhikuhi pinepine ai me he lā lā. Me nā pemphigus vulgaris, ulcer i hana ke wehe ʻia nā vesicle a hui i nā liona nui. ʻAʻole like me ka stomatitis, kahi i hōʻike ʻia e ka erosion me kahi uhi keʻokeʻo, he poni ʻulaʻula a me kahi ʻālohilohi o nā pemphigus ulcer. Ke hoʻopili ʻia ka larynx e pemphigus, lilo ka leo o ka mea maʻi i mea kani;
• erythematous ʻike ʻia ke ʻano o ka pemphigus e ka ʻoiaʻiʻo e hoʻopili nui i ka ʻili o ka umauma, ka maka, ka ʻāʻī a me ke poʻo. ʻO nā rashes o kahi ʻano seborrheic me nā palena maopopo i uhi ʻia me nā ʻāpala ʻeleʻele a melemele paha; ke wehe ʻia, hōʻike ʻia ka ʻaʻai. ʻAʻole maʻalahi kēia ʻano pemphigus i ke kuhi, no laila hiki ke hoʻokau ʻia ka erythematous form ma mua o hoʻokahi makahiki, a inā he exacerbation, hōʻike paha ia i nā ʻōuli o kahi hua ʻole;
• lau-lau - hiki i nā huhū o kahi erythema-squamous ke hana ma nā wahi i hoʻopili ʻia o ka ʻili, a laila wehe ʻia nā puka me nā paia lahilahi, e hana ana i ka ʻaʻai, kahi e hoʻomaloʻo a lilo i uhi ʻia me nā crust lamellar. ʻO kēia ʻano pemphigus, ma ke ʻano he lula, hoʻopili i ka ʻili, hohola koke nā huʻa liʻiliʻi ma luna o ka ʻili olakino, i kekahi mau hihia, e hōʻino ʻia nā membrane mucous;
• mea kanu hōʻike ʻia ke ʻano e nā huʻa i ka wahi o nā pale o ka ʻili, ma kahi o nā huʻa, hoʻoneʻe ʻia me kahi pilau putrid a me nā ʻano pura purulent ma luna o ka manawa.

Hoʻohui ʻia me nā huehue ma ka ʻili a me nā membrane mucous, he mau ʻōuli maʻamau nā mea maʻi me ka pemphigus:

1. 1 luhi;
2. 2 ua hōʻemi a nalowale paha o ka makemake;
3. 3 paona kaupaona me ka hoʻonui ʻana o ka meaʻai;
4. 4 hiamoe.

Nā pilikia

Me ka lapaʻau untimely a pololei ʻole paha, hoʻolaha ʻia nā huʻa i loko o ke kino, hui a hana i nā leona nui. ʻO ka holo pemphigus kahi pilikia nui me ka ʻili. Hoʻopili nā liona ʻili i ke ola o ka mea hoʻomanawanui, ʻaʻole hiki i ka mea hoʻomanawanui ke neʻe maʻamau. Ke hoʻopili ʻia nā erosions, ʻo ka pyoderma ka mea maʻalahi maʻamau.^[4]… Hiki nō hoʻi ka hoʻolaha ʻana o nā hana hoʻāhu i nā mea o loko, ma muli o ka hopena e ulu ai ka phlegmon a me ka niumonia.

Ma ka ʻaoʻao o ENT, e ulu paha ka lohe pepeiao ma ke ʻano he komplication o pemphigus; lanakila ʻo mycoses ma waena o nā pilikia dermatological. Hōʻike ʻia nā pilikia o ka ʻōnaehana cardiovascular ma ke ʻano o ka ischemia, angina pectoris a me microangiopathy.

ʻOi aku ka kiʻekiʻe o ka make o nā mea maʻi me ka pemphigus - a hiki i ka 15% o nā mea maʻi e make i loko o 5 mau makahiki ma hope o ka hoʻomaka ʻana o ka maʻi.

Kāohi

Ma ke ʻano he mea pale e pale ai i ka hoʻomohala ʻana o pemphigus, pono ʻoe:

• hoʻololi pinepine i ka lilina moe;
• hoʻololi i ka lole komo ma lalo i kēlā me kēia lā;
• mālama pono i nā maʻi maʻi o ka ʻili;
• e hoʻoneʻe i ka poʻe hana me ka pele pustular;
• ka mana ʻōnaehana o kahi dermatologist;
• e kaupalena i ka lawe ʻana i ka paʻakai, ka momona a me nā kōpaka;
• e nānā i ka heluhelu ʻana i ke kō glucose a me ke kaomi koko;
• mālama pono i nā lula o ka hoʻomaʻemaʻe pilikino.

Hoʻomaʻo i ka lāʻau mainstream

Lōʻihi a paʻakikī hoʻi ka mālama ʻana ʻo Pemphigus. Hōʻike ʻo Pemphigus i ka lāʻau lapaʻau paʻakikī:

1. 1 ʻōnaehana ʻōnaehana;
2. 2 kūloko kūloko;
3. 3 ʻenehana extracorporeal.

Hoʻopili ka lāʻau kūloko i ka mālama ʻana i ka ʻili i hoʻopili ʻia me ka hoʻōla a me nā hamo hormonal a me ka hoʻoinu ʻana o nā erosions me nā painkillers.

Hoʻopili ka lāʻau Extracorporeal i ka hoʻohana ʻana o hemodialysis a me plasmaphoresis.

ʻO ke kumu nui o ka mālama ʻana pemphigus ʻo ia ka hoʻōla hormonone. Kauoha ʻia ka mea hoʻomanawanui i nā huaale, a hāʻawi ʻia nā mea maʻi i ka haukapila i nā corticosteroids i loko o ke kino. Pono e mālama pono ʻia ka lāʻau lapaʻau, mai ka lawe ʻana i nā lāʻau hormonal hiki i nā hopena ʻino:

• kaumaha;
• nā maʻi hiamoe;
• hypertension;
• momona, ʻoiai me ka papa haʻahaʻa-kalori;
• maʻi ʻaʻano steroid-type;
• pīhoihoi nui o ka ʻōnaehana ʻōiwi;
• maʻi ahulau.

Me kahi exacerbation, hōʻike ʻia nā lāʻau e kāohi i ka ʻōnaehana pale. ʻO nā mea maʻi me ka pemphigus koʻikoʻi e pono ai e pani hou i ka plasma. I nāʻano koʻikoʻi o nā maʻi pilikino, kuhikuhi ʻia ka immunoglobulin i loko o ke kino.

I mea e pale aku ai i ka maʻi ma hope o ka wehe ʻana i nā palapū, ua kauoha ʻia nā lāʻau ʻalopika no nā mea maʻi me ka pemphigus. Hoʻopili ʻia nā lole i pulu ʻia i ka jelly ʻaila i nā ulcer a me nā wahi e ninini ana. I ka hihia o ka exacerbation, paipai ʻia e ʻaʻahu i nā kapa kūpale i hana ʻia mai nā lole maoli.

E nānā!

ʻAʻole kuleana ke alakaʻi no nā hoʻāʻo e hoʻohana i ka ʻike i hāʻawi ʻia, a ʻaʻole ia e hoʻohiki ʻaʻole e hōʻeha iā ʻoe iho. ʻAʻole hiki ke hoʻohana i nā mea e kuhikuhi ai i ka lāʻau lapaʻau a hana i kahi kuhi. E nīnau mau i kāu kauka loea.