Hōʻike ākea o ka maʻi
He maʻi koko hoʻoilina maʻamau kēia e ʻike ʻia ai nā pilikia pili pū ke koko.
Nā ʻano hemophilia
He maʻi maʻi kūpilikiʻi ʻo Hemophilia kahi e loli ai kekahi ʻāpana ma ka X chromosome. Kaukaʻi ʻia i ka ʻāpana i hoʻololi ʻia, hoʻokaʻawale ʻia kekahi ʻano maʻi ʻokoʻa. ʻEkolu ʻano o Hemophilia: A, B, C.
- ʻAno A -ʻAʻohe protein kūikawā i loko o ke koko: antihemophilic globulin, mea VIII o ke kāpili ʻana o ke koko. Hana ʻia kēia kīnā kīnā i 85% o nā mea maʻi a manaʻo ʻia he kūlana.
- ʻAno B -ʻAʻole lawa ka hana IX, no ka mea i hoʻopōpilikia ʻia ke kaʻina hana o ka plugina lua.
- E kikokiko C - hemophilia o kēia ʻano ma muli o ka lawa ʻole o ka mea coagulation XI. ʻAno C he ʻano kākaʻikahi loa ia, kahi i hoʻopili nui ʻia i nā Iudaio Ashkenazi. Hiki i nā wahine a me nā kāne ke maʻi pū me ia. I kēia manawa, ua kāpae ʻia kēia ʻano mai ka hoʻohālikelike ʻana ma muli o ka ʻokoʻa loa o kāna mau hōʻailona mai nā ʻano ʻelua.
Nā kumu o ka maʻi
ʻO ke kumu nui o ka hoʻomohala ʻana o ka hemophilia i manaʻo ʻia he ʻano hoʻoilina.
Kākaʻikahi loa nā hihiahemophilia kūlohelohe". Kū koke ʻo ia, ʻoiai ʻaʻole i loaʻa ka ʻohana i kēia maʻi ma mua. Ma hope iho, hoʻouna ʻia kēia ʻano hemophilia i ka hana kuʻuna - ma ka pae genetical. ʻAʻole ʻike ka poʻe loea i nā kumu kūpono no ka ulu ʻana o ka maʻi. Manaʻoʻiʻo lākou he hoʻololi hou kēia o kēia.
Ka likelihood o ka hoʻoilina hemophilia
ʻO ka hapa nui e ʻeha nā kāne i kēia maʻi. Hoʻouna ʻia ka maʻi i ke kāne kāne i ke ʻano recessive (pili i ka X chromosome). Inā hoʻoilina ke keikikāne i ka makuahine X - chromosome, ʻaʻole i loaʻa iā ia ka hemophilia. Hāʻawi ʻia nā wahine i ke kuleana o ka "conductor" a i ʻole ka lawe halihali, akā aia paha nā hoʻokoe. Inā maʻi ka makuakāne me ka hemophilia, a he lawe ka makuahine, a laila he kaikamahine paha kā kēlā mau mākua e ʻeha nei i kēia maʻi. Ma ka hōʻuluʻulu, ma kahi o 60 mau hihia i hoʻopaʻa inoa ʻia i ka honua kahi i ʻeha ai nā kaikamahine i ka hemophilia, a ʻaʻole nā mea lawe.
Aia he 3 mau ʻano like o ka lawe ʻana o ka hemophilia
- 1 ʻO ka makuahine ka mea lawe i ka ʻāpana, akā he kāne olakino ka makuakāne. I kēia hihia, hiki i nā hopena 4, me ka likelika he 25%. He keikikāne olakino a he kaikamahine olakino paha, hānau kahi keikikāne maʻi a kaikamahine paha lawe.
- 2 Maikaʻi ka makuahine, maʻi ka makua kāne me ka hemophilia. I kēia kūlana, e olakino nā keikikāne āpau, a lilo nā kaikamahine āpau i mau halihali.
- 3 ʻO ka makuahine ka mea lawe i ka ʻohana, a maʻi ka makuakāne. I kēia ʻano ʻokoʻa, hiki i nā hopena 4: he keikikāne olakino, he kaikamahine maʻi, he keikikāne maʻi, a he kaikamahine lawe. He ikaika like ko kēlā me kēia hopena.
Nā ʻōuli o ka hemophilia
I ka hemophilia, ʻike ʻia ke kahe nui ʻana o ke kahe, e kū pinepine ʻia me nā wahi ʻokoʻa i nā wā ʻeha like ʻole, nā kaʻina hana olakino (ʻo ia hoʻi nā injection intramuscular a me nā hana ʻoki), a ke lawe ʻia nā niho.
He paʻakikī loa ka Gum a i ʻole nā ihu e kū. Eia kekahi, e hoʻomaka paha ke kahe ʻana o ke koko.
Me nā hōʻeha liʻiliʻi a me nā ʻeha, ua hoʻokumu ʻia kahi hematoma nui.
ʻO ka hiʻona nui o hemophilia ka intra-articular kahe ʻana ke koko - hemarthrosis. Ke kū lākou i ka ami, pilikia ka neʻe, kū ka pehu. Hele pū kēia mau mea me ka ʻehaʻeha loa. Ma hope o ka mua o ke kahe ʻana o ke koko, pau ke koko i ka hui i kāna iho a hoʻihoʻi ʻia ka hana o ka ami. Akā me ka hana hou ʻana, hana nā clots ma ka capsule hui a me ka cartilage, i uhi ʻia me nā mea hoʻopili. Hoʻolālā ʻo Ankylosis ma muli o ia ʻano hana.
ʻO kekahi hōʻailona koʻikoʻi i ka hemophilia ka hopena, hoʻolohi ʻia ke ʻano o ke kahe ʻana. ʻAʻole wehe koke ke kahe ʻana ma hope o ka ʻeha, akā ma hope o kekahi manawa. Loaʻa kēia i ka ʻoiaʻiʻo i ka mua ua kāpae ʻia ke kahe e nā platelet, ʻaʻole hoʻololi ʻia ka hoʻohui ʻana. Hiki iā ia ke lawe mai 6 a 12 mau hola ma mua o ka wehe ʻana o ke kahe ʻana - pili ia i ka nui o ka maʻi.
Aia paha he koko i ka mimi a i ʻole nā feces. ʻO ka hōʻailona paʻakikī a make loa hoʻi o ka hemophilia kahi hemorrhage i ka iwi kuamoo a i ʻole ka lolo.
No nā keiki, lōʻihi paha ka lōʻihi o ka hoʻomohala ʻana o ka hemophilia. Pili kēia i nā pēpē i hānai ʻia e ka makuahine. ʻOiaʻiʻo, i ka waiū umauma he mau mea kūikawā e kākoʻo i ka hiki i ke koko ke kāpili maʻamau. No laila, ʻo ka lōʻihi o ka hānai ʻana o ka makuahine i ka pēpē, ʻike ʻia nā hōʻailona mua.
Nā ʻano hemophilia
Ma muli o ke koʻikoʻi o ka maʻi, 3 mau ʻano o ka hemophilia e hoʻokaʻawale ʻia.
- RџSЂRё ʻoluʻolu hiki ke kahe ʻia ka hemophilia i ka wā o ke kahakaha ʻana a ma hope paha o ka trauma ʻeha. I ke koko, loaʻa ka mea coagulation i kahi nui o 5-25%.
- RџSЂRё papa haʻahaʻa hemophilia kāwili mea i loko o ke koko i loko o ka pae o 1 i ka 5%. Hiki ke ʻike ʻia nā hōʻailona hōʻailona mua i ka wā ʻōpio. No kēia palapala, pili ke kahe ʻana i ke koko i nā ʻeha kūpono, a me nā ʻeha liʻiliʻi, kū nā hematomas koʻikoʻi.
- RџSЂRё ʻano koʻikoʻi nā maʻi, loaʻa i ke koko kahi mea coagulation ma lalo o 1%. I kēia hihia, hōʻike ʻo hemophilia iā ia iho i nā mahina mua o ke ola - i ka wā o ka niho, hāmama ke kahe, a i nā hoʻāʻo mua e hele, ʻike ʻia nā hematomas koʻikoʻi a nui (i ka wā o ke kolo, no ka snagging o nā mea a hāʻule paha).
ʻO nā mea maʻi kaulana a me nā mea lawe o hemophilia
ʻO Queen Victoria ka mea i lawe nui ʻia ʻo hemophilia i ka mōʻaukala. Eia kekahi, ʻaʻole ia e hilinaʻi ʻia no nā kumu i lilo ai ʻo ia i mea. Ma hope o nā mea āpau, ma mua o kēlā, ʻaʻohe mea o ka ʻohana i ʻeha i kēia maʻi. Aia he 2 mana.
ʻAe ka mea mua i hiki i kona makuakāne ke lilo i kāne ʻē aʻe i loaʻa i ka hemophilia, a ʻaʻole na ke Duke o Kent Edward Augustus. Akā ʻaʻohe hōʻike palapala.
No laila, ua hāʻawi ʻia i kahi mana ʻelua - ua hoʻololi ʻo Victoria i kāna mau gen. ʻO ia, ua loaʻa iā ia kahi ʻano "spontan" o hemophilia. A e like me ke kumu maʻamau, ua hoʻoilina ʻia ka hemophilia e kāna keiki - ke Duke o Albany, Leopold a me kekahi moʻopuna a me nā moʻopuna.
Ua manaʻo ʻia ʻo Hemophilia ka maʻi o nā mōʻī. Ua wehewehe ʻia kēia mea e ka ʻoiaʻiʻo ma mua, no ka mālama pono ʻana i ka inoa, ʻae ʻia ka male ʻana me nā ʻohana pili. No laila, ʻo ka likelika o ka loaʻa ʻana o nā keiki maʻi i ka hale hoʻokolokolo ua hoʻonui nui ʻia.
ʻO ke kaʻao o ka hemophilia
Aia kekahi kaʻao e hiki i ke kanaka me ka hemophilia ke kahe i ka make ma ka ʻino iki o ka ʻili. ʻAʻole mamao loa kēia ʻōlelo, a no ia poʻe, ʻaʻohe mea weliweli a ʻoki liʻiliʻi hoʻi i kahi makaʻu.
ʻO nā mea pōpilikia nā hana ʻokiʻoki, huki i nā niho, nā lāʻau āpau a me ke kahe ʻana o ke koko i loko o nā mākala a me nā kīʻaha koko, e kū nei ma muli o nā paia nāwaliwali nāwaliwali i nā mea maʻi.
Nā meaʻai olakino no ka hemophilia
Me ka hemophilia, ʻaʻohe o nā kulekele papaʻai pono e mālama pono ʻia.
No ka hoʻihoʻi ʻana i ke koko a hoʻomaikaʻi i ka hoʻopili ʻana, pono ia e ʻai i ka meaʻai i piha ka paʻakai o ka phosphore, ka calcium, nā huaora A, B, C, D. ʻO ka mea nui ka hāʻawi ʻana i ke kino i ka nui o ka huina K. ka coagulation (coagulation) wikamina.
Hiki ke kiʻi ʻia ka wikamina K ma ka ʻai ʻana i ka milo, letus, aniani, kāloti, maiʻa, kālika, kukama, ʻōmato, pears, ʻāpala, kāpelu (ʻo ia hoʻi ka broccoli, kāpiki keʻokeʻo, cauliflower), nā peppers wela, nā soybeans, hua moa, ka waiū, aila pata , ʻoka, turnip top, keleka.
I mea e hoʻomaikaʻi ai i ke ʻano o ke koko, hoʻāla i ka hemoglobin, hoʻoikaika i nā paia o nā kīʻaha koko a hoʻohaʻahaʻa i nā pae kolesterol, pono ia e hoʻopili i ka papaʻaiʻai, nā iʻa momona, nā hua citrus, nā nati, nā pomeraite, avocado, nā beets, ka wai cranberry, ka meli , buckwheat porridge, kāloti, ʻāpala a me nā wai beet ...
Pono e inu ʻia ka wai Beet me ka wai kāloti a i ʻole ka wai ʻāpala. ʻO ka mea mua, pono e hoʻoheheʻe ʻia i 1 a 1, a laila e hoʻoliʻiliʻi mālie i ka dilution a hoʻonui i ka nui o ka wai beet.
Eia kekahi, hiki iā ʻoe ke inu i ka wai hoʻomaʻemaʻe, kī ʻōmaʻomaʻo, tī me nā currants, viburnum a i ʻole nā hua ʻalani, rosehip decoction.
Lapaʻau kuʻuna no ka hemophilia
I mea e pale ai i ke kahe ʻana, hiki i nā mea maʻi ke lawe i nā hua hua waina, decoctions o ka ʻupena dioecious, yarrow, astragalus, Japanese Sophora, kahu ʻeke, arnica, coriander, witch hazel, dandelion root. ʻO kēia mau mea kanu lāʻau e kōkua i ka hoʻoikaika ʻana i nā paia o nā kīʻaha koko, e hoʻonui i ke kāpili ʻana o ke koko a hoʻomaikaʻi i ka maikaʻi o ke koko.
Pono ʻoe e lawe i ka aspirin palena a me nā lāʻau lapaʻau ʻokiʻoki koko, nā mea e hiki ai ke kahe i ke kahe.
Nā meaʻai weliweli a hoʻopōʻino hoʻi no ka hemophilia
- nā meaʻai momona (loaʻa ka nui o ka kolesterol, a eia kekahi, pale nā momona i ka lawe ʻana o ka calcium, a he mea nui ia no ke kaulike pūnaewele.
- palai, paʻakai, ipu puhi ʻia (ʻo kēia meaʻai nā mea i hoʻololi i ka hoʻohui ʻana o ke koko ʻaʻole no ka maikaʻi, ʻo ia ke kumu e loli ai nā kino i ke kino holoʻokoʻa i ka wā e hiki mai ana);
- ʻalekohola, soda momona, nā mea inu ikehu (hoʻopau lākou a make wai i nā hunaola koko, ʻo ia ke kumu e hiki ʻole ai i ke koko ke kū i kāna mau hana);
- ʻO ka meaʻai wikiwiki, ka momona momona, nā huahana semi-hoʻopau, nā meaʻai hikiwawe, mālama i nā meaʻai hiki ke hoʻopaʻa ʻia, nā sausages, nā meaʻai a me nā mea ʻono, a me nā meaʻai me nā mea hoʻohui meaʻai like ʻole (ʻo kēia mau "huahana" he mau pūhui kaumaha ʻaʻole hiki ke hoʻohana ʻia nā kīʻaha koko e hānai i ke kino kanaka. , akā, hoʻohui lākou i nā mea ʻawaʻawa i ke kino me kēia mau mea ʻino.
E nānā!
ʻAʻole kuleana ke alakaʻi no nā hoʻāʻo e hoʻohana i ka ʻike i hāʻawi ʻia, a ʻaʻole ia e hoʻohiki ʻaʻole e hōʻeha iā ʻoe iho. ʻAʻole hiki ke hoʻohana i nā mea e kuhikuhi ai i ka lāʻau lapaʻau a hana i kahi kuhi. E nīnau mau i kāu kauka loea.