ʻO Thrombocythemia kahi hoʻolaha o nā platelet koko, me ka hopena o ka hoʻonui ʻia o ka thrombosis (ke koko koko). Hoʻomaopopo ʻia ia e ka hāpana koko a i ʻole ka biopsy iwi o ka iwi. Mālama ʻia me nā aspirins a i ʻole nā ​​anti-platelets.

Definition

ʻO Thrombocythemia kahi hui o nā maʻi koko. Pili nui lākou i nā platelet koko, nā hunaola i hana ʻia e ka iwi iwi a nona ke kuleana e hoʻopili i ke koko (e paʻa paʻa).

I ka wā o ka thrombocythemia ka hana ʻana o nā hunaola kūpuna i ka momona o ka iwi he mea ʻole ia, alakaʻi ia i ka hoʻonui ʻia ʻana o nā huna ākea platelet. Eia nō naʻe, ko lākou kuleana ʻo ka hui pū ʻia o ke koko, alakaʻi kēia hoʻolaha i ka hoʻonui ʻana i ka makaʻala o nā kīʻaha koko: thrombosis.

I kahi liʻiliʻi, hiki i ka thrombocythemia ke hopena i ka kahe koko me ka ʻole o ka ʻeha.

Nā pilikia i ka mea maʻi

ʻO ia ka hopena o ka thrombocythemia e makaʻu ai. Noho ka Thrombosis i kumu nui o ka make. ʻO ka awelika ola o kahi kanaka me ka thrombocythemia i hana ʻole ʻia he 12 a 15 mau makahiki, akā ʻokoʻa ka loli ma muli o ka nui o ka thrombosis.

ʻO ka hopena nui ʻē aʻe ka helehelena o ka hemorrhages, (ʻoi loa i ka ʻili a i ʻole i nā membrane mucous). Hiki i ka thrombositosis ke kumu i nā nosebleeds, gums, bruising mai nā puʻupuʻu liʻiliʻi, a i ʻole ke koko i ka mimi.

Nā kumu o ka thrombocythemia

ʻElua mau ʻano thrombocythemia:

• Nā hopena, i ka hopena i ke ao Hiki i kēia maʻi ke hana i nā ʻano like ʻole, e like me ka maʻi, ka mumū, ke koʻikoʻi koʻikoʻi, ka ʻole o ka hao i ke koko, a i ʻole kahi tumo.
• ʻO nā mea nui, ma 10 a 20% o nā hihia, i hōʻike ʻia me ke kumu ʻole i hoʻokumu ʻia. ʻO lākou kahi o ka myeloproliferative syndromes.

Kuhikuhi iā ia

ʻO ke kuhi o ka thrombocythemia hana ʻia e ka hāpana koko. Loiloi ʻia ka paepae ma kahi pae platelet i ʻoi aku ma mua o 450 ma ka microliter, me nā palena maʻamau. No laila hiki ke hana maʻalahi ʻia kēia kuhi e kahi hoʻokolohua koko maʻamau i ka wā o kahi hāʻawi koko a i ʻole ka loiloi olakino.

Hiki ke hana i nā hoʻāʻo genetic e hōʻike i ka maʻi.

I kekahi manawa pono ka biopsy iwi pūliki (hōʻiliʻili laʻa) e hoʻāʻo no ka hana ʻana o ka cell stem.

Nā mea pilikino

Hoʻopili nui ka Thrombocythemia i nā mākua ma waena o nā makahiki 50 a me 70, a me nā wahine ʻōpio. ʻO nā mea maʻi ma luna o 60 mau makahiki i ka nui o ka makaʻu inā loaʻa iā lākou ka mōʻaukala o ka thrombosis (ke koko) a i ʻole nā ​​hōʻeha koko ʻē aʻe. Eia nō naʻe, ʻaʻole kahi helu platelet kiʻekiʻe i hōʻailona o ka makaʻu.

ʻAʻohe hōʻailona maoli o thrombocythemia, akā kū kekahi mau kuhi:

• ʻO ka hoʻā ʻana o ke ahi, ʻulaʻula, kani ʻana i ka wēlau o ke kino (nā lima, nā wāwae), a i ʻole ka loaʻa ʻana o ka manamana lima anu.
• ʻEha ma ka umauma
• ʻIke o nā kiko ma ka hihiʻo
• Nāwaliwali o ke kino, ʻūpā
• Headaches
• Kahe ʻana o ka hū

ʻO ke ala ʻoi loa ka nānā ʻana i ka helu o ka platelet o kou koko i ka wā o nā loiloi maʻamau. Ua koho ʻia he hapa o ka thrombositosis ʻike ʻia me ka ʻole o ka mea hoʻomanawanui e hoʻopiʻi ana i nā ʻōuli.

Aspirin

ʻO ka hapa nui o nā hihia o ka thrombocythemia e mālama ʻia me ka aspirin, no nā mea anti-coagulant, e hōʻemi i ka makaʻi o ka thrombosis, a ʻo ia hoʻi e hōʻoluʻolu i nā ʻōuli.

Pāʻali kūloko

Lawe ʻia nā lāʻau e like me hydroxyurea a me nā anagrelides a i ʻole interferon-alpha a hiki i ka helu ʻana o ka platelet koko i ka maʻamau.

ʻO Thrombacytaphérèse

I kahi ulia pōpilikia, no ka laʻana inā kiʻekiʻe ka helu platelet, hiki ke hana i ka thrombacytapheresis. ʻO ke kumu o ka hana e huki i ke koko o ka mea maʻi, e wehe i nā platelet koko ma mua o ka hoʻoiho ʻana iā ia me ka ʻole o nā pā.

Hiki ke hele pū me nā hihia ʻoi loa me kahi transplant cell stem no kahi ʻōpio.

ʻOiai he maʻi ʻole ka maʻi i nā manawa he nui, pono ʻoe e maʻa i ka lawe pinepine ʻana i kēia ʻano lāʻau anti-coagulant no ke koena o kou ola.

ʻAʻole like me ka thrombocythemia reactive, i ʻike ʻia ma hope o kahi maʻi ʻē aʻe, he kumu ko nā mea nui e paʻakikī loa e hoʻomaopopo, a no laila ʻaʻohe pale pono.